BACKGROUND AND PURPOSE The cause of intracranial bleeding in moyamoya disease patients is still unknown. To identify factors that contribute to bleeding, we assessed the angiographic findings of moyamoya disease patients. METHODS We examined angiograms obtained from 107 moyamoya patients; 70 manifested ischemic and 37 had hemorrhagic lesions. Patients with intracerebral aneurysms or both hemo...

Moyamoya disease is infrequently associated with intracranial aneurysms arising from the circle of Willis vessels or from "peripheral" branches of choroidal and meningeal vessels. We present a rare case of a moyamoya-related aneurysm arising along the dural junction of multiple meningeal branches from the external carotid artery causing intracerebral hemorrhage. Endovascular coil embolization o...

Four adult female patients with moyamoya vessels are described. Hypertension and hyperlipidaemia were discovered in three patients. Vessels similar to moyamoya vessels were seen in the orbital and cortical collateral vessels as well as in the basal ganglia region. Attention should now be paid to the aetiological rather than the descriptive aspects of the disorder. An empirical trial of corticos...

Isolated middle cerebral artery (MCA) stenosis in young patients with no other medical condition may be a unique pathologic entity with a benign long-term course. Generally, moyamoya disease shows a progression of stenosis from internal cerebral artery (ICA) to other intracranial vessel. A 26-year-old woman was admitted for choreic movements of the right arm and leg. Brain magnetic resonance im...

Moyamoya Disease – Case Report. Moyamoya disease is a more common disease in Asian population and well discussed since 1957. Because of the continuously increasing population of people with migration background, this disease is getting a topical subject in European countries. Characterized by occlusion of the distal carotid arteries, it is a progressive disease with a fragile network of basal c...

Cerebral arteriovenous malformations (AVMs) are associated with a variety of alterations in the angioarchitecture of the feeding arteries and draining veins [1-3]. Between January 1985 and December 1988 we examined the angiograms of 97 patients with cerebral AVMs to assess their potential for endovascular treatment. Two patients showed occlusion of major vessels and an associated moyamoya pheno...

Objectives: -Discuss and understand the anesthetic considerations for a patient with complicated sickle cell disease who is undergoing general anesthesia. -Discuss and understand the pathophysiology of moyamoya disease. -Discuss and understand the preoperative, intraoperative, and postoperative management of patients with moyamoya disease. -Discuss and understand the implications of general ane...

Neurofibromatosis type 1 (NF1) is the most prevalent autosomal dominant genetic disorder among humans. NF1 vasculopathy is a significant but underrecognized complication of the disease, affecting both arterial and venous blood vessels of all sizes. Moyamoya syndrome is a cerebral vasculopathy that is only rarely observed in association with NF1, particularly in the pediatric age range. Herein, ...

Moyamoya syndrome is the secondary form of intracranial arterial occlusive diseases that produces collateral vessels from the base of brain. We report a case of Moyamoya syndrome developing in association with Graves thyrotoxicosis; as a result of its rapid progression and severe global ischemia, it was ultimately fatal. Because of the rarity of this association, we reviewed the literature in a...

AGS: Aicardi-Goutieres syndrome CTCL: cutaneous T-cell lymphoma SAMHD1: SAM domain and HD domaincontaining protein 1 SAMS: stroke, aneurysm, moyamoya, and stenosis SLE: systemic lupus erythematosus INTRODUCTION Mutations in the SAMHD1 (SAM domain and HD domainecontaining protein 1) gene are implicated in SAMS (stroke, aneurysm, moyamoya, and stenosis) association, also described as AicardiGouti...