نتایج جستجو برای: neurometabolic

تعداد نتایج: 416  

Journal: :Neurophotonics 2017
Patrick M Schaefer Diana Hilpert Moritz Niederschweiberer Larissa Neuhauser Sviatlana Kalinina Enrico Calzia Angelika Rueck Bjoern von Einem Christine A F von Arnim

Alterations of cellular bioenergetics are a common feature in most neurodegenerative disorders. However, there is a selective vulnerability of different brain regions, cell types, and even mitochondrial populations to these metabolic disturbances. Thus, the aim of our study was to establish and validate an in vivo metabolic imaging technique to screen for mitochondrial function on the subcellul...

Journal: :The New England journal of medicine 2016
Maja Tarailo-Graovac Casper Shyr Colin J Ross Gabriella A Horvath Ramona Salvarinova Xin C Ye Lin-Hua Zhang Amit P Bhavsar Jessica J Y Lee Britt I Drögemöller Mena Abdelsayed Majid Alfadhel Linlea Armstrong Matthias R Baumgartner Patricie Burda Mary B Connolly Jessie Cameron Michelle Demos Tammie Dewan Janis Dionne A Mark Evans Jan M Friedman Ian Garber Suzanne Lewis Jiqiang Ling Rupasri Mandal Andre Mattman Margaret McKinnon Aspasia Michoulas Daniel Metzger Oluseye A Ogunbayo Bojana Rakic Jacob Rozmus Peter Ruben Bryan Sayson Saikat Santra Kirk R Schultz Kathryn Selby Paul Shekel Sandra Sirrs Cristina Skrypnyk Andrea Superti-Furga Stuart E Turvey Margot I Van Allen David Wishart Jiang Wu John Wu Dimitrios Zafeiriou Leo Kluijtmans Ron A Wevers Patrice Eydoux Anna M Lehman Hilary Vallance Sylvia Stockler-Ipsiroglu Graham Sinclair Wyeth W Wasserman Clara D van Karnebeek

BACKGROUND Whole-exome sequencing has transformed gene discovery and diagnosis in rare diseases. Translation into disease-modifying treatments is challenging, particularly for intellectual developmental disorder. However, the exception is inborn errors of metabolism, since many of these disorders are responsive to therapy that targets pathophysiological features at the molecular or cellular lev...

2012
Vicki L Mahan

Studies in animal models show that the primary mechanism by which heme-oxygenases impart beneficial effects is due to the gaseous molecule carbon monoxide (CO). Produced in humans mainly by the catabolism of heme by heme-oxygenase, CO is a neurotransmitter important for multiple neurologic functions and affects several intracellular pathways as a regulatory molecule. Exogenous administration of...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 2007
Baowang Li Ralph D Freeman

The relationships between neural and metabolic processes in activated brain regions are central to the interpretation of noninvasive imaging. To examine this relationship, we have used a specialized sensor to measure simultaneously tissue oxygen changes and neural activity in colocalized regions of the cat's lateral geniculate nucleus (LGN). Previous work with this sensor has shown that a decre...

2017
Ali G. Hamedani Daniel R. Gold

Eye movement abnormalities are among the earliest clinical manifestations of inherited and acquired neurodegenerative diseases and play an integral role in their diagnosis. Eyelid movement is neuroanatomically linked to eye movement, and thus eyelid dysfunction can also be a distinguishing feature of neurodegenerative disease and complements eye movement abnormalities in helping us to understan...

Journal: :Stroke 2002
Michael D Hill Philip A Barber Andrew M Demchuk Nancy J Newcommon Andrea Cole-Haskayne Karla Ryckborst Laurel Sopher Allison Button William Hu Mark E Hudon William Morrish Richard Frayne Robert J Sevick Alastair M Buchan

BACKGROUND Intravenous alteplase for acute ischemic stroke is least efficacious for patients with proximal large-artery occlusions and clinically severe strokes. Intra-arterial therapy has the theoretical advantage of establishing a neurovascular diagnosis and high symptomatic artery patency rate but the disadvantage of requiring extra time and technical expertise. A combination of these two ap...

2014
Parveneh KARIMZADEH Farzad AHMADABADI Narjes JAFARI Fakhreddin SHARIATMADARI Hamid NEMATI Adel AHADI Sanaz KARIMI DARDASHTI Mehrdad MIRZARAHIMI Zahra DASTBORHAN Javad ZARE NOGHABI

OBJECTIVE Phenylketonuria is one of the most common metabolic disorders and the first known cause of mental retardation in pediatrics. As Screening for phenylketonuria (PKU) is not a routine neurometabolic screening test for neonates in Iran, many PKU cases may be diagnosed after developing the clinical symptoms. One of the findings of PKU is myelination disorders, which is seen as hypersignal ...

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