A 34 year old women was admitted to the hospital with a 9 year history of intermittent haemoptysis associated with increasing breathlessness. A working diagnosis of lymphangioleiomyomatosis was made, based on clinical, radiological and histological findings. Three years later, the patient was admitted to hospital with worsening haemoptysis, which rapidly progressed and resulted in death from ma...

Benign intra-abdominal cystic masses in infancy are fairly uncommon and their etiopathogenesis, histology and clinical presentation differ significantly. Our aim is to report our experience in their treatment in order to discuss the best diagnostic and treatment modality. The medical records of 5 children (2M, 3F) with cystic intraabdominal masses referred to our hospital between November 2012 ...

In 1994, we published a rare case report of a left sided pneumothorax caused by a mesenchymal cystic hamartoma (MCH) in this journal (Thorax 1994;49:1175–6). After a follow-up of 23 years, the same patient was referred for a left sided pain and thoracic mass at age 36 years. At age 14 years, a left sided thoracotomy was performed for recurrent pneumothorax followed by lobectomy of the left lowe...

Primary myxomas and myxosarcomas of the lung are very rare. Stout studied in 1948 the records of Columbia University and the cases reported in the world literature and was able to collect 140 cases but there were no myxomas arising from the lung or pleura. Miller and Jackson (1954) reported a case of myxosarcoma of the lung and Barkley and Cardozo (1957) published another case of myxomatous tum...

Hamartoma es una masa desorganizada, benigna, compuesta por tejidos y células nativas de sitio anatómico afectado. El hamartoma lingual infantil un tumor benigno e infrecuente que generalmente se descubre en la niñez. No conoce patogenia, pero parece estar relacionada a persistencia restos embrionarios mesenquimales. Se presenta el caso paciente con patología región lingual.

Nasal chondromesenchymal hamartoma has characteristic clinicopathological features and it is accepted as the upper airway analogue of mesenchymal hamartoma of the chest wall. It is a rare lesion and only 31 cases have been reported in the English literature until 2014. In this article, a 13-year-old nasal chondromesenchymal hamartoma case is presented, which is the first nasal chondromesenchyma...

Retrorectal tumors are rare lesions in adults, which remains a difficult diagnostic and management problem. The purpose of this study was to evaluate the results of surgical management of retrorectal tumors in our institution. In a retrospective study, a consecutive series of patients who underwent surgical excision of a retrorectal tumor were identified from a database. Medical records, radiol...