Phacomatosis pigmentovascularis is a rare syndrome characterized by the coexistence of a pigmented nevus and a cutaneous vascular malformation. We report a 5-year-old boy with all the typical findings of phacomatosis pigmentovascularis type Ia. Although its existence according to the traditional classification has been questioned, this case represents a very rare association of a capillary vasc...

Two children presented with symptoms suggestive of a vascular ring. Barium esophagrams in each case showed a posterior impression caused by a retroesophageal aortic arch. Angiographic studies defined a rare form of vascular ring resulting from an ascending left-sided aorta, a descending right-sided aorta and a right-sided ligamentum arteriosum. At surgery, the diagnosis was confirmed and the an...

Echocardiography revealed systemic artery to pulmonary venous fistula, a rare vascular anomaly, in a 20-month-old girl, and multislice computed tomography angiography (CTA) was performed to rule out congenital heart disease. Normal bronchial connection and pulmonary vasculature were observed in the lung. The fistula drained through the left inferior pulmonary vein to the left atrium leading to ...

We present an anomaly of the subscapular vascular tree that has not been previously reported. The serratus anterior pedicle originated directly from the subscapular vessels from the proximal third of the axillary artery. The thoracodorsal vessels arose separately, directly from the distal third of the axillary vessels. This vascular pattern was not encountered in any previous patient in our ser...

IMPORTANCE Pediatric imaging carries the risk of radiation exposure. Children frequently undergo computed tomography with angiography (CTA) for findings on bronchoscopy with limited knowledge regarding the necessity of such imaging. OBJECTIVE To report our experience with all pediatric patients at our institution over an 8-year period with airway symptoms warranting bronchoscopy followed by C...

A rare case of neonatal Ebstein's anomaly with circular shunting was reported. A two-stage surgical procedure was performed, and the outcome was good. Razook JD. Repair of Ebstein's anomaly in the symptomatic neonate: an evolution of technique with 7-year follow-up. Rapid two-stage Starnes procedure for a symptomatic neonate with Ebstein anomaly. Ebstein's anomaly appearing in the neonate. A ne...