The acoustic rearing environment can alter central auditory coding properties, yet altered neural coding is seldom linked with specific deficits to adult perceptual skills. To test whether developmental hearing loss resulted in comparable changes to perception and sensory coding, we examined behavioral and neural detection thresholds for sinusoidally amplitude modulated (sAM) stimuli. Behaviora...

School-based hearing screening programs have been commonplace in the United States since the 1960’s. Historically, the enrollment of children in the public school system afforded the first opportunity to have access to a large population of children in order to screen for hearing disorders. Such programs were primarily designed to identify hearing losses that necessitated medical referral and t...

Paget's disease is a common bone remodeling disorder that typically begins with excessive bone resorption in the elderly. Bilateral progressive hearing loss is the most frequently encountered complication of Paget's disease. The types of hearing loss identified by audiometry are conductive, sensorineural, or both. However, the precise mechanism of hearing loss remains unclear, and the treatment...

BACKGROUND Stickler syndrome is a connective tissue disorder characterized by ocular, skeletal, orofacial and auditory defects. It is caused by mutations in different collagen genes, namely COL2A1, COL11A1 and COL11A2 (autosomal dominant inheritance), and COL9A1 and COL9A2 (autosomal recessive inheritance). The auditory phenotype in Stickler syndrome is inconsistently reported. Therefore we per...

The use of the distraction test as a screen for hearing loss in infancy was reviewed in the Bristol and District Health Authority. Inaccuracies in data recording were found which challenged the screening and referral rates produced by the National Child Health Computer. Representative samples of children failing the distraction test and children needing hearing aids were followed up through the...

INTRODUCTION Otosclerosis is an osteodystrophy of the labyrinthine capsule producing conductive hearing loss. If the process invades the cochlea, a sensorineural hearing loss usually takes place. The cochlear implant is a good alternative in these patients. OBJECTIVE To ascertain the behaviour of cochlear implantation in otosclerosis. MATERIAL AND METHODS We reviewed a database of 250 patie...

The purpose of this investigation was to examine the effects of prolonged monaural amplification on the suprathreshold speech-recognition scores in the unaided ears of 46 persons with bilateral essentially symmetric and conductive hearing impairment and aided ears of 46 other persons with bilateral essentially symmetric and conductive hearing impairment. All subjects were less than 50 years of ...

[This corrects the article on p. 92 in vol. 8, PMID: 26045905.].

A three-generation family with Saethre-Chotzen syndrome and an isolated case are presented. The proband presented with conductive hearing loss. His mother and grandmother showed minor features of the syndrome including conductive hearing loss. Symptoms of the craniosynostosis syndromes can include stapes ankylosis, a fixed ossicular chain in a too small epitympanum, and small or even absent mas...

In the developed world, there are currently more than 100 million people afflicted with hearing loss. In the United States and European Community alone, there are an estimated 21 million people with significant conductive hearing loss, whilst there are over 90 million suffering from moderate to severe sensorineural hearing loss. Of these, more than 65 million hearing-impaired persons are withou...