UNLABELLED Abstract PURPOSE We present the clinical, paraclinical and therapeutic features in a patient with secondary congenital aphakia. METHODS A 2-year-old patient, diagnosed with congenital rubella syndrome including sensorineural deafness, congenital heart disease, intellectual disability, microcephaly, microphthalmia, and congenital cataract, presented to our clinic for the surgical ...

OBJECTIVE Poor growth is a common complication in infants with congenital heart disease. There has been much focus on low birth weight as having increased risk of adverse outcomes following neonatal heart surgery. In this study, we examined whether preoperative nutritional status, measured by admission weight-for-age z score, was associated with postoperative clinical outcome. DESIGN Retrospe...

OBJECTIVE Ambient hypoxia impairs the airway epithelial Na transport, which is crucial in lung edema reabsorption. Whether chronic systemic hypoxemia affects airway Na transport has remained largely unknown. We have therefore investigated whether chronic systemic hypoxemia in children with congenital heart defect affects airway epithelial Na transport, Na transporter-gene expression, and short-...

patients and methods sixty children aged between 2 and 12 years, and scheduled for on-pump surgery due to a congenital heart disease were randomly assigned into two groups. oral midazolam (0.5 mg/kg up to 15 mg per patient) and dexmedetomidine (2 µg/kg) were administered 45 minutes pre-anesthesia. children’s anxiety, mask acceptance behavior, hemodynamic measures, and cardiopulmonary outcomes w...

In congenital cardiac surgery, intracardiac repair procedures like ventricular septal defect (VSD), atrioventricular and tetralogy of fallot (TOF) are associated with conduction system injury. Fewer cases reported describing life threatening complication late post-operative complete heart block. We reporting 2 patients who presented block after managed by permanent pacemaker placement in AFIC C...

With the advances in congenital cardiac surgery and postoperative care, an increasing number of children with complex congenital heart disease now reach adulthood. There are already more adults than children living with a congenital heart defect, including patients with complex congenital heart defects. Among these adults with congenital heart disease, a significant number will develop ventricu...