ease secondary to congenital heart disease. I woud like to show you two children, 0110 of whom was considered to have congenital heart disease and was found at postmortem examination to have primary pulmonary disease. In the other case the child was considered to have primary pulmonary disease and then was found to have pulmonary disease secondary to heart disease. The first case is that of a g...

We report the case of a 17-year-old male with Marfanoid habitus who presented with deep cyanosis, haematemesis, dyspnoea and platypnoea. He had oesophageal varices, indicating portal hypertension, with mildly deranged liver function. His arterial blood gas (ABG) revealed hypoxia and orthodeoxia. Contrast-enhanced echocardiography with agitated saline and a 99m Technetium macro-aggregated albumi...

In the past two or three years our attention has been drawn to a condition in newborn babies which, although not particularly uncommon, does not seem to be widely known and which may give rise to needless anxiety. The doctor is usually called to see a baby which is born spontaneously but after birth appears to be grossly cyanosed. A nurse has usually put the baby into an oxygen tent. On two or ...

Methemoglobinemia is a dyshemoglobinemia characterized by cyanosis and reduced oxygen saturation with increased methemoglobin values. The etiology may be congenital or acquired, the latter being more common. We report case of full-term neonate who presented transient methemoglobinemia caused mutation in gamma chain fetal hemoglobin.