We describe a female infant with the cervical vertebral fusion (Klippel-Feil) syndrome whom we recognized at birth because of her short neck, restriction of cervical movement, and low posterior hairline. X-ray examination showed anomalies of C1, and between C2-3 and C3-4; thus, we classified her as type II, with variable cervical fusion. At 24 months she was small and manifested hearing deficie...

Klippel Feil Syndrome (KFS) is a congenital malformation which has a failure of segmantation of cervical somites in the 8th weeks of gestation and fusion at least two cervical segments. It is described as the triad of short neck, low posterior hairline and decreased range of neck motions. Especially decreased range of neck motions lead many anesthesiologists to difficult airway management. Dexm...

hypoxemia under certain conditions. However, the relationship between pulmonary anesthetic administration and HPV remains controversial. In conclusion, global effects of inhalation induction with sevoflurane at high concentrations may cause oxygen desaturation in lungs that are normally ventilated with 100% oxygen, potentially resulting in global inhibition of HPV. However, these conditions may...

The Klippel-Feil syndrome (KFS) has been reported to be associated with intracranial neoplasms, most frequently epidermoid or dermoid cysts. To our knowledge, however, patients who present with a posterior fossa dermoid cyst (DC) and KFS are extremely rare with only 24 previously reported cases in the English literature worldwide. Therefore, we present the first report of a patient with a crani...

Also, evidence for "formes frustes" of Duanes' syndrome in other family members in the forni of pareses of oculomotor muscles other than the lateral rectus or of slight narrowing of the palpebral fissure on adduction, has been reported by FranSois and de Vos (I958) and by Orlowski, Krych, and MIichniowska-Leonowicz (I96I). Most of the above observations have been confined to single sibships, or...

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