نتایج جستجو برای: hepatic iron overload

تعداد نتایج: 251907  

Journal: :Clinical science 1980
C Selden C A Seymour T J Peters

The activities and subcellular distribution of enzymes implicated in the protection of cells from free-radical mediated damage were determined in liver biopsy specimens from control and iron-overloaded patients. 2. There was a small but insignificant decrease in the activity of glutathione reductase in patients with secondary iron overload due to multiple transfusion therapy for thalassaemia ma...

Journal: :Blood 1995
D Mathieu A Rahmouni P Villeneuve M C Anglade H Rochant N Vasile

Magnetic resonance (MR) imaging is a method of choice for assessing vascular patency and parenchymal iron overload. During the course of paroxysmal nocturnal hemoglobinuria (PNH), it is clinically relevant to differentiate abdominal vein thrombosis from hemolytic attacks. Furthermore, the study of the parenchymal MR signal intensity adds informations about the iron storage in kidneys, liver, an...

2013
Alessia Pepe Antonella Meloni Giuseppe Rossi Liana Cuccia Giuseppe Domenico D’Ascola Michele Santodirocco Paolo Cianciulli Vincenzo Caruso Maria Antonietta Romeo Aldo Filosa Lorella Pitrolo Maria Caterina Putti Angelo Peluso Saveria Campisi Massimiliano Missere Massimo Midiri Letizia Gulino Vincenzo Positano Massimo Lombardi Paolo Ricchi

BACKGROUND Due to the limited data available in literature, the aim of this multi-centre study was to prospectively compare in thalassemia major (TM) patients the efficacy of combined deferiprone (DFP) and deferoxamine (DFO) regimen versus either DFP and DFO in monotherapy by cardiovascular magnetic resonance (CMR) over a follow up of 18 months. METHODS Among the first 1135 TM patients in the...

Journal: :Journal of medical genetics 1999
A P Walker D F Wallace J Partridge A B Bomford J S Dooley

Beta2-microglobulin was investigated in atypical haemochromatosis patients not homozygous for the C282Y mutation of HFE (OMIM *235200), because the HFE protein binds beta2-microglobulin, and in mice beta2-microglobulin gene knockout causes hepatic iron overload. Six unrelated patients with atypical haemochromatosis were studied. Five patients had normal HFE coding sequence and the sixth was het...

Journal: :The Egyptian journal of immunology 2010
Olfat M Hendy Maha Allam Alif Allam Mohamed Hamdy Attia Salwa El Taher Mervat Mohii Eldin Amal Ali

Beta-thalassemia is an inherited anemia in which synthesis of the hemoglobin beta-chain is decreased. Clinical features of beta-thalassemia include variably severe anemia and iron overload due to increased intestinal iron absorption, which may result in damage to vital organs. The hepatic peptide; hepcidin is a key regulator of iron metabolism in mammals. The present study aimed to determine th...

Journal: :The American journal of clinical nutrition 2011
Xuan Zheng Tao Jiang Hong Wu Dezeng Zhu Ling Wang Rui Qi Min Li Changquan Ling

BACKGROUND Emerging scientific evidence has disclosed a correlation between iron metabolism and type 2 diabetes (T2D). OBJECTIVE The objective of this study was to test the hypothesis that body iron stores are higher in a Chinese population with altered glucose homeostasis. DESIGN Serum iron, ferritin, and soluble transferrin receptor concentrations were measured in 298 subjects, including ...

Journal: :Liver International 2021

Background Iron status has been linked with impaired glucose metabolism (IGM), type 2 diabetes mellitus (T2DM) and the metabolic syndrome (MetS), but role of hepatic steatosis or iron overload on these associations remains uncertain. Methods We analysed data from 2310 participants without known T2DM population-based Study Health in Pomerania (SHIP-TREND, Germany) through logistic regression mod...

Journal: :Pathology 2012
Itty M Nadakkavukaran Eng K Gan John K Olynyk

Hereditary haemochromatosis (HH) is a common autosomal recessive disorder of iron overload in Caucasian populations. Clinical manifestations usually occur in individuals homozygous for the C282Y mutation in the HFE gene product and who have developed significant iron loading. Current screening methods can detect affected individuals either prior to or early during disease evolution, enabling ea...

2016
Jung-Heun Ha Caglar Doguer Xiaoyu Wang Shireen R. Flores James F. Collins

Iron-copper interactions were described decades ago; however, molecular mechanisms linking the two essential minerals remain largely undefined. Investigations in humans and other mammals noted that copper levels increase in the intestinal mucosa, liver and blood during iron deficiency, tissues all important for iron homeostasis. The current study was undertaken to test the hypothesis that dieta...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2000
R E Fleming M C Migas C C Holden A Waheed R S Britton S Tomatsu B R Bacon W S Sly

Hereditary hemochromatosis (HH) is a common autosomal recessive disorder characterized by excess absorption of dietary iron and progressive iron deposition in several tissues, particularly liver. Liver disease resulting from iron toxicity is the major cause of death in HH. Hepatic iron loading in HH is progressive despite down-regulation of the classical transferrin receptor (TfR). Recently a h...

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