1 Barst RJ. Experience and reason [editorial]. Chest 2000; 117:2–5 2 Klings ES, Hill NS, Ieong MH, et al. Systemic sclerosisassociated pulmonary hypertension: shortand long-term effects of epoprostenol (prostacyclin). Arthritis Rheum 1999; 42:2638–2645 3 Klings ES, Ieong MH, Simms RW, et al. Long-term intravenous epoprostenol therapy for pulmonary hypertension associated with systemic sclerosis...

how to cite this article: karimzadeh p, ahmadabadi f, jafari n, jabbehdari s, alaee mr, ghofrani m, taghdiri mm, tonekaboni sh. biotinidase deficiency: a reversible neurometabolic disorder (an iranian pediatric case series). iran j child neurol. 2013 autumn; 7(4):47- 52.   objective biotinidase deficiency is one of the rare congenital metabolic disorders with autosomal recessive inheritance. if...

The Shoulder Pain and Disability Index (SPADI) was developed to measure current shoulder pain and disability in an outpatient setting. The SPADI contains 13 items that assess two domains; a 5-item subscale that measures pain and an 8-item subscale that measures disability. There are two versions of the SPADI; the original version has each item scored on a visual analogue scale (VAS) and a secon...

Nuclear pore complexes (NPCs) provide the sole gateway for the exchange of material between nucleus and cytoplasm of interphase eukaryotic cells. They support two modes of transport: passive diffusion of ions, metabolites and intermediate-sized macromolecules, and facilitated, receptor-mediated translocation of proteins, RNA, and RNPs complexes. It is generally assumed that both modes of transp...

1) From the Department of Biochemistry, Albert Einstein College of Medicine, 1300 Morris Park Avenue, Bronx, NY 10461, USA 2) Department of Cell Biology, Harvard Medical School, 240 Longwood Avenue, Boston, MA 10115, USA 3) present address: Kavli Institute of NanoScience, Department of BioNanoScience, Technical University Delft, Lorentzweg , 2628 CJ Delft, The Netherlands 4) present address: De...

ATP-BINDING CASSETTE TRANSPORTER A1 MEDIATES THE BENEFICIAL EFFECTS OF THE LIVER-X-RECEPTOR AGONIST GW3965 ON OBJECT RECOGNITION MEMORY AND AMYLOID BURDEN IN APP/PS1 MICE James J. Donkin, Sophie Stukas, Veronica Hirsch-Reinshagen, Dhananjay Namjoshi, Anna Wilkinson, Sharon May, Jeniffer Chan, Jianjia Fan, Jon Collins, and Cheryl L. Wellington From Department of Pathology and Laboratory Medicine...