A neonate with pulmonary atresia and an intact ventricular septum with a tripartite right ventricle was successfully treated by percutaneous balloon dilatation of the pulmonary valve. This was facilitated by previous laser valvotomy with a hot tip Trimedyne laser wire. There were no major complications. Four weeks later the patient was discharged home on no medication with peripheral oxygen sat...

A multistage plan and multidisciplinary approach are the keys to successful repair in patients with pulmonary atresia (PA) with ventricular septal defect (VSD) and major aortopulmonary collateral arteries (MAPCAs). In this article, we present a multidisciplinary approach adopted to treat a patient with PA with VSD and MAPCAs associated with left pulmonary artery interruption.

To cite: Sharma A, Malhi AS, Kumar S, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/ bcr-2016-216265 DESCRIPTION A 3-month-old girl child presented with a history of respiratory distress, rapid breathing and mild cyanosis since birth. Auscultation revealed systolic murmur (3/6) in the right parasternal and upper left parasternal area. ECG showed right axis de...

BACKGROUND Cardiac magnetic resonance (CMR) imaging is an important clinical tool for serial follow-up of patients with congenital heart disease, but normative data for great vessel dimensions in pediatric subjects are scarce. We investigated the ascending aortic (AO) and main pulmonary artery dimensions in normal children and young adults in comparison with a cohort of patients with repaired t...

Five patients have had the common features of pulmonary atresia or severe stenosis associated with a septal defect and a coronary artery-to-pulmonary artery (CA-PA) fistula. Four had pulmonary valvular atresia, and one had severe pulmonary stenosis. In all five, the CA-PA fistula contributed the principal component of the pulmonary blood flow. Cyanosis, continuous murmur, right ventricular hype...

Aneurysm of the left sinus of Valsalva is rare, and there is only one previous report of rupture into the pulmonary artery. This report describes a patient with valvular pulmonary atresia and ventricular septal defect in whom a portion of his pulmonary blood flow was supplied by an aortopulmonary tunnel arising from a left sinus of Valsalva aneurysm. The surgical implications of precise definit...

We report a Kawashima procedure (total cavopulmonary shunt) successfully carried out for asplenia syndrome, pulmonary atresia, and major aortopulmonary collateral arteries. At the age of 8, the patient underwent staged bilateral unifocalizations using confluent central pulmonary arteries concomitant with bilateral modified Blalock-Taussig shunts. As the result of an interrupted inferior vena ca...

A case of pulmonary valve atresia with intact ventricular septum' with long survival in the absence of a patent ductus arteriosus, is presented. The patient, alive at 21 years of age, has the anterior descending branch of the left coronary artery originating from the pulmonary artery. Thus, the pulmonary blood supply is obtained from the right coronary artery via intercoronary anastomoses. No s...

A12-month-old child was evaluated for pulmonary atresia with ventricular septal defect. Assessment of the whole arterial pulmonary arborization was first done by angiography. This examination revealed that the left lung received vascularization by the native pulmonary artery via a central shunt performed during the neonatal period and by 2 aortopulmonary collateral arteries. The positions of th...

In mitral atresia with a closed or narrowly patent foramen ovale, anomalous pulmonary venous connexions may occur that function as collateral pathways for the return of pulmonary venous blood to the heart. In 2 cases (Edwards and DuShane, 1950; Lucas et al., 1962), although all the pulmonary veins' connected normally, an anomalous channel-termed a levo-atriocardinal veinformed the collateral pa...