نتایج جستجو برای: rhabdoid tumor

تعداد نتایج: 428329  

2009
Meena Sidhu

Primitive neuroectodermal tumor (PNET) / medulloblastoma (MB) are the most common malignant central nervous tumors of the first decade of life. Atypical teratoid / rhabdoid tumor (ATT / RT) is a tumor of infancy and childhood although occasional cases have also been described in adults. ATT/RT has a characteristic histopathological, immunocytochemical and ultrastructural features. ATT /RT is a ...

2015
Alex Rabinovich Leora Witkowski Ruthy Shaco-Levi Mihai Meirovitz Martin Hasselblatt William D. Foulkes

•The third case of pure primary malignant rhabdoid tumor of the ovary (MRTO) is described•SMARCA4 and SMARCB1 genetic analysis and immunohistochemistry are necessary for correct diagnosis of MRTO•MRTO and small cell carcinoma of the ovary, hypercalcemic type are essentially the same and should be treated as such.

Journal: :Pathology, research and practice 2013
Kaishi Satomi Yukio Morishita Yoshihiko Murata Aya Shiba-Ishii Masato Sugano Masayuki Noguchi

Atypical teratoid/rhabdoid tumor (AT/RT) is a rhabdoid tumor of the central nervous system comprising a mixture of small round cells and mesenchymal and/or epithelial elements, showing mutation of the SMARCB1 gene or SMARCA4 gene. The epidermal growth factor receptor (EGFR) is one of the tyrosine kinase receptors whose overexpressed protein plays important roles in the malignant characteristics...

Journal: :Proceedings 2014
Varsha Podduturi Molly M Campa-Thompson Xin J Zhou Joseph M Guileyardo

Malignant rhabdoid tumors (MRT) of the kidney are rare in children and even less common in adults, with only six previously reported adult cases. We present the case of a 60-year-old man with an MRT arising in the left kidney with extensive pulmonary micrometastases and thromboembolism resulting in thrombotic pulmonary microangiopathy (pulmonary tumor embolism syndrome). MRT is an extremely agg...

Journal: :The Journal of neuroscience : the official journal of the Society for Neuroscience 2014
Natalia Moreno Christin Schmidt Julia Ahlfeld Julia Pöschl Stefanie Dittmar Stefan M Pfister Marcel Kool Kornelius Kerl Ulrich Schüller

SMARCA4 (BRG1) and SMARCB1 (INI1) are tumor suppressor genes that are crucially involved in the formation of malignant rhabdoid tumors, such as atypical teratoid/rhabdoid tumor (AT/RT). AT/RTs typically affect infants and occur at various sites of the CNS with a particular frequency in the cerebellum. Here, granule neurons and their progenitors represent the most abundant cell type and are know...

2013
Ryan Horazdovsky J. Carlos Manivel Edward Y. Cheng

Purpose. Malignant rhabdoid tumor (MRT) is an uncommon tumor that rarely occurs outside of renal and central nervous system (CNS) sites. Data from the literature were compiled to determine prognostic factors, including both demographic and treatment variables of malignant rhabdoid tumor, focusing on those tumors arising in extra-renal, extra-CNS (ER/EC MRT) sites. Patients and Methods. A system...

2016
Jocelyn P. Wong Jason R. Todd Martina A. Finetti Frank McCarthy Malgorzata Broncel Simon Vyse Maciej T. Luczynski Stephen Crosier Karen A. Ryall Kate Holmes Leo S. Payne Frances Daley Patty Wai Andrew Jenks Barbara Tanos Aik-Choon Tan Rachael C. Natrajan Daniel Williamson Paul H. Huang

Subunits of the SWI/SNF chromatin remodeling complex are mutated in a significant proportion of human cancers. Malignant rhabdoid tumors (MRTs) are lethal pediatric cancers characterized by a deficiency in the SWI/SNF subunit SMARCB1. Here, we employ an integrated molecular profiling and chemical biology approach to demonstrate that the receptor tyrosine kinases (RTKs) PDGFRα and FGFR1 are coac...

2013
GUANGNING ZHAO REN NA YUMING YANG RUIFA HAN

Malignant rhabdoid tumors of the kidney (MRTKs) are extremely rare. Pure MRTKs in adult patients are particularly rare and have not been previously reported in China. Due to the non-specific clinical symptoms, it is difficult but also essential to be able to give a definite diagnosis. The present study reports a case of pure adult malignant rhabdoid tumor in a patient's left kidney with charact...

2017
Arnault Tauziède-Espariat Julien Masliah-Planchon Laurence Brugières Stéphanie Puget Christelle Dufour Pascale Schneider Annie Laquerrière Thierry Frebourg Damien Bodet Emmanuèle Lechapt-Zalcman Gaëlle Pierron Olivier Delattre Pascale Varlet Franck Bourdeaut

About one third of patients with rhabdoid tumors (RT) harbor a heterozygous germline variant in SMARCB1. Molecular diagnosis therefore keeps a crucial place in the diagnosis of RT, and genetic counseling should be systematically recommended. However, immunohistochemistry has progressively replaced molecular tools to assess the status of SMARCB1 in tumors; the necessity of analyzing SMARCB1 stat...

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