background: coronary artery disease is one of the most common causes of morbidity and mortality in developed countries. atherosclerosis begins in early childhood and progresses through life. with advances in pediatric cardiology, the prevalence of congenital heart disease in adults has increased in relation to children. a great deal of research has been conducted on serum glucose and lipid conc...

background: we sought to assess right ventricular (rv) systolic and diastolic functions via tissue doppler imaging (tdi) in order to discriminate right-to-left (bidirectional) from left-to-right intracardiac shunts. methods: a tissue doppler velocity study via doppler echocardiography was performed in 20 patients with left-to-right shunt (without evidence of significant pulmonary hypertension) ...

left ventricular non-compaction cardiomyopathy is a rare congenital cardiomyopathy that affects both children and adults. since the clinical manifestations are not sufficient to establish diagnosis, echocardiography is the diagnostic tool that makes it possible to document ventricular non-compaction and establish prognostic factors. we report a 47-year-old woman with a history of dilated cardio...

a case of multiple pulp stones, a supernumerary tooth and a congenitally missed tooth accompanied by several developmental dental anomalies concurrently affect- ing the upper and lower anterior teeth in an iranian healthy girl is reported. devel- opmental tooth abnormalities are usually found in conjunction with certain diseases or conditions. in the present case, although the patient had consa...

background: chylothorax is a rare but serious postoperative condition with a high rate of morbidity and may lead to the mortality of children undergoing congenital heart disease (chd) surgery. this study evaluated the specific surgical procedures associated with the higher risk of postoperative chylothorax. methods: w e assessed 435 cases undergoing chd surgery between april 2003 and may 2006. ...

background: congenital adrenal hyperplasia (cah, the inherited inability to synthesize cortisol) is one of the most common (1 in 10000 to 1 in 15000) autosomal recessive disorders. more than 95% of cases of cah are caused by 21-hydroxylase deficiency (21-ohd). females with severe, classic 21-ohd are exposed to excess androgens prenatally and are born with virilized external genitalia. most pati...

introduction: the lack of adequate blood perfusion through different organs of the body, including the brain and skull, can be caused by any type of circulation abnormality. the purpose of this study is to compare cephalometric indices between infants under the age of 12 months who have congenital heart disease (chd) and normal infants. materials and methods: this case-control study was carried...

purpose: to evaluate refractive state in patients with unilateral congenital nasolacrimal duct obstruction. methods: in this descriptive prospective study, patients with unilateral congenital nasolacrimal duct obstruction scheduled for surgery were enrolled over a period of two years (2007-2009). cycloplegic refractive error in both eyes was measured under anesthesia before surgery (probing, si...

congenital generalized lipodystrophy (cgl) is a rare and progressive disorder (1 in 12 milion). common clinical manifestations are lipoatrophy, acromegaloid feature, acanthosis nigricans, hyperlipidemia, diabetes mellitus or abnormal glucose tolerance test.â rarely fatty liver and cirrhosis is seen. the highest number reported in literature is 8 cases from brazil and 6 cases from scandinavia, r...

objective(s) carbamazepine (cbz) is an antiepileptic drug that is used widely for the treatment of epileptic seizures. neural tube defects (ntds), growth retardation, and nail hypoplasia are the most common features of teratogenic effects of this drug. the purpose of this study was to examine the effect of vitamin b6 on the developmental toxicity of cbz on mice. materials and methods sixty balb...