The Abernethy malformation is a rare congenital malformation defined by the presence of an extrahepatic portosystemic shunt. Although most patients are asymptomatic, clinical encephalopathy is present in 15% of cases. We present a patient with type 2 Abernethy malformation, hyperammonemia, and encephalopathy. Shunt closure was performed successfully using interventional angiography; however, hy...

The most common type of vascular malformation is the venous malformation and these are occasionally associated with phleboliths. We report a case of a 45 year old woman with intraoral venous malformation with phleboliths.

UNLABELLED Primary lymphedema and capillary malformation are independent vascular malformations that can cause overgrowth of the lower extremity. We report a series of patients who had both types of malformations affecting the same leg. The condition is unique but may be confused with other types of vascular malformation overgrowth conditions (eg, Klippel-Trenaunay and Parkes Weber). METHODS ...

Klippel-Trenaunay syndrome (KTS) is a rare complex vascular with limb hypertrophy. KTS diagnosed if at least two of the three features capillary malformation, venous and soft tissue and/or bone overgrowth are present. Of these, malformation (i.e., port-wine stain) most commonly observed feature but may be absent in atypical KTS. We herein report case unilateral

BACKGROUND Sequestration with associated cystic adenomatoid malformation is rare. A study was undertaken to determine whether pulmonary sequestration associated with congenital cystic adenomatoid malformation has a more favourable natural history than that of sequestration without associated cystic adenomatoid malformation. METHODS An outline of the postnatal work up leading to the management...

natural vibration analysis of plates represents an important issue in engineering applications. in this paper, a new and simplify method for vibration analysis of circular and rectangular plates is presented. the design of an effective robust controller, which consistently attenuates transverse vibration of the plate caused by an external disturbance force, is given. the dynamics of the plate i...

Prostatic ductal adenocarcinomas may arise either in large primary periurethral prostatic ducts or in the peripheral prostatic ducts. Ductal adenocarcinomas are composed of tall columnar cells arranged in cribriform, papillary, solid, single glands, and PIN-like patterns. Other than the prostatic intraepithelial neoplasia (PIN)-like ductal pattern, which behaves like Gleason pattern 3, ductal a...

The pancreas is a complex organ comprised of three critical cell lineages: islet (endocrine), acinar, and ductal. This review will focus upon recent insights and advances in the biology of pancreatic ductal cells. In particular, emphasis will be placed upon the regulation of ductal cells by specific transcriptional factors during development as well as the underpinnings of acinar-ductal metapla...

BACKGROUND Female genital malformations represent miscellaneous deviations from normal anatomy. This study aimed to explore the clinical characteristics of patients who underwent surgery for genital tract malformations at Peking Union Medical College Hospital (PUMCH) during a 31-year period. METHODS We retrospectively reviewed surgical cases of congenital malformation of the female genital tr...

The production of bile is an essential function of the liver. It contains cholesterol, bile acids, pigments and electrolytes, and their concentration is modified when the bile transits through the biliary tract. The bile is produced by the hepatocytes and is secreted into the bile canaliculi. These canaliculi are delineated by the apical membrane of the hepatocytes and are connected to the netw...