Abstract Hepatic epithelioid hemangio-endothelioma (EHE) is a rare, often misdiagnosed malignancy of vascular origin. We describe case 36-year-old, who presented with burning sensation in his chest on exercise and was believed to have bilobar intrahepatic cholangiocarcinoma. After receiving chemotherapy partial response, the patient underwent staged resection modified ALPPS (associating liver p...