Biliary cystadenomas are rare tumors of the bile ducts most commonly presenting as large right liver lobe lesions. These are usually slow-growing and mostly benign. They commonly present with abdominal pain. On physical exam an abdominal mass can be identified occasionally. Walls of biliary cystadenomas appear thicker than simple cysts, with soft tissue nodules and enhancing septations on CT or...

Biliary atresia (BA) is a rare disease characterised by a biliary obstruction of unknown origin that presents in the neonatal period. It is the most frequent surgical cause of cholestatic jaundice in this age group. BA occurs in approximately 1/18,000 live births in Western Europe. In the world, the reported incidence varies from 5/100,000 to 32/100,000 live births, and is highest in Asia and t...

The term portal biliopathy (PB) is used to describe the biliary abnormalities associated with portal hypertension. Between 5% and 30% of patients with PB develop biliary obstruction. We report on a patient with extrahepatic biliary obstruction caused by PB that was successfully managed with an intrahepatic segment 3 bypass. The traditional surgical approach for a patient with extrahepatic bilia...

children who are operated for biliary atresia by the kasai procedure have approximately 30% chance of survival for 5 years. in an attempt to define the role of this operation for biliary atresia, the surgery records of the past 15 years were reviewed. the aim of this study was to assess the benefits achieved from this operation in infants with biliary atresia. this study was conducted in the de...

OBJECTIVES This study investigated the association between cancer of the extrahepatic biliary tract and exposure to endocrine-disrupting compounds. METHODS Altogether 183 men with histologically confirmed carcinoma of the extrahepatic biliary tract and 1938 matched controls were interviewed between 1995 and 1997 in the frame of an international multicenter case-control study in six European c...

gallbladder and biliary tree is low compared with the many parenchymal hepatic conditions that occur in animals. Diseases of the extrahepatic biliary system are often confused with other intraabdominal disorders because their course and clinical signs are similar. Diseases that require surgery of the extrahepatic biliary system in dogs are primarily acquired and include extrahepatic biliary tra...

Background Chronic liver diseases (CLD) in children represent a growing health problem with significant morbidity and mortality. This study aimed to define the clinicopathological pattern of pediatric CLD in Sohag University Hospital, Sohag,Upper Egypt. Materials and Methods A total of 151children with CLD were included in a prospective hospital-based study from June 2014 to May 2018. Cases of...

Upper abdominal ultrasonic examination demonstrated dilated bile ducts in eight patients with no history of jaundice and a normal serum bilirubin. All were proven subsequently to have extrahepatic biliary obstruction. It is important to recognise that ultrasound may be more sensitive than serum bilirubin in the diagnosis of extrahepatic biliary obstruction.

Biliary atresia and choledochal cyst have the similar clinical presentation in infants. Herein, we report a case that presented with prolonged hyperbilirubinemia and abdominal distension and diagnosed as choledochal cyst. At surgery, in addition to a large choledochal cyst, biliary atresia was also encountered.

We describe the rare instance of concomitant biliary atresia and alpha-1-antitrypsin deficiency and the first documented successful portoenterostomy in this scenario. The potential for dual pathology must be recognized and underscores that prompt diagnosis of biliary atresia, despite concomitant alpha-1-antitrypsin deficiency, is essential to afford potential longstanding native liver function.