Gorlin-Goltz syndrome or basal cell nevus syndrome is an autosomal dominant syndrome characterized by skeletal anomalies, numerous cysts observed in the jaw, and multiple basal cell carcinoma of the skin, which may be accompanied by falx cerebri calcification. Basal cell carcinoma is the most commonly skin tumor with slow clinical course and low metastatic potential. Its concomitance with Gorli...

The first dental case report of a patient with focal dermal hypoplasia syndrome (FDHS) is presented. A review of signs and symptoms of FDHS is presented along with newly reported oral findings. This patient apparently is the first person with FDHS to have an absent sternum and the fifteenth person reported with confirmed osteopathia striata. Carious lesions can be difficult to restore in FDHS d...

This case series reports the clinical presentation and management of multiple odontogenic keratocysts (OKCs) in patients with Gorlin Goltz syndrome non-syndromic patients. Eight presented features keratocyst at department Oral Maxillofacial Surgery. The diagnosis was confirmed following clinical, radiographic histopathological examination. Initially OKC on an incisional biopsy. Major minor crit...