نتایج جستجو برای: hexosaminidase

تعداد نتایج: 835  

Journal: :Journal of medical genetics 1979
R Bernstein B Dawson R Kohl T Jenkins

Cytogenetic studies on a retarded girl showed a complex S;15 translocation, karyotype 45,X,-15,+t(X15). The translocation X chromosome was non-randomly partially inactivated, the inactivation being mainly confined to the X segment and in some cells only to the X long arm. Gene marker studies failed to show anomalous segregation of the hexosaminidase A gene or any other gene markers tested.

Journal: :iranian journal of allergy, asthma and immunology 0
reza safaralizadeh department of biochemistry, national institute of genetic engineering and biotechnology, tehran, ira zahra-soheila soheili department of biochemistry, national institute of genetic engineering and biotechnology, tehran, ira abdolkhaleg deezagi department of biochemistry, national institute of genetic engineering and biotechnology, tehran, ira zahra pourpak immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, ir shahram samiei iranian blood transfusion organization research center, tehran, iran mostafa moin immunology, asthma and allergy research institute, tehran university of medical sciences, tehran, ir

fcεri, the high affinity receptor for ige plays a critical role in triggering the allergic reactions. it is responsible for inducing mast cell degranulation and deliberation of allergy mediators when it is aggregated by allergen and ige complexes. fcεri on the mast cells consists of three subunits; α chain directly binds ige, β chain and dimmer of γ chains together mediate intracellular signali...

Journal: :The Biochemical journal 1988
M J Buckmaster A L Ferris B Storrie

Upon detergent or hypo-osmotic lysis of CHO-cell postnuclear supernatants or isolated lysosomes at pH 4.8, the lysosomal enzymes beta-hexosaminidase, beta-galactosidase, alpha-fucosidase and cathepsin C were readily pelleted, whereas the exogenous marker, long-term-internalized horseradish peroxidase, was not. Salt or pH elevation greatly decreased lysosomal-enzyme pelletability. The results su...

ژورنال: ارمغان دانش 2019

Background and aim: Tachyx is a rare autosomal recessive and neurological disorder caused by glycosfenolipid accumulation (GM2 ganglioside) in cell lysosomes. The accumulation of GM2 ganglioside is due to the mutation in the beta-hexose aminase gene (HEXA), which reduces the activity and deficiency of the HEXA enzyme. The aim of this study was to report 2 cases of T.Sax disease.   Case report:...

2012
Susanne C. Diesner Cornelia Schultz Xueyan Wang Gerda Ratzinger Philipp Starkl Vera Assmann Kristina Kreiner Franziska Roth-Walter Isabella Pali-Schöll Erika Jensen-Jarolim Franz Gabor Eva Untersmayr

rendered background IgE levels only. In accordance, sera of OVA mice which permitted mast cell degranulation upon OVA trigger in a specific b-hexosaminidase release assay, whereas sera of OVA-AAVLP mice did not contain anaphylactogenic antibodies. In an in vivo anaphylaxis experiment, upon intravenous OVA challenge OVA-immunized mice presented significant drop of body temperature, whereas AAVLP...

2012
Wendy Ramírez González Alexis Labrada Virgilio Bourg Bárbara González Damarys Torralba Arelis Más Quintero Oliver Pérez Miriam Lastre

rendered background IgE levels only. In accordance, sera of OVA mice which permitted mast cell degranulation upon OVA trigger in a specific b-hexosaminidase release assay, whereas sera of OVA-AAVLP mice did not contain anaphylactogenic antibodies. In an in vivo anaphylaxis experiment, upon intravenous OVA challenge OVA-immunized mice presented significant drop of body temperature, whereas AAVLP...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید