We describe the first Marfan syndrome case of non-traumatic bilateral radial artery aneurysms in the anatomical snuff box. A 74-year-old woman with Marfan syndrome had a pulsatile mass in her bilateral anatomical snuff box. The color Doppler ultrasonography showed an aneurysm of radial artery located in the bilateral anatomical snuff box. Resection of the right radial artery aneurysm was comple...

Rupture of thoracic aortic aneurysms and/or dissections is not rare, occurring in approximately 0.6% of all medicolegal autopsies. Most forensic pathologists are aware of the association between thoracic aortic aneurysms/dissections and trauma, atherosclerosis, inflammation and Marfan syndrome. In this report, we discuss a familial form of thoracic aortic dilatation and/or dissection that is di...

People with Marfan syndrome present with a range of health problems that require specialised nursing, medical and surgical care. They face many challenges throughout their lives - some of which may be life-threatening - and require continuing support and education from a specialist team. Nurses play a pivotal role in the care of people with Marfan syndrome and their families, encompassing not o...

Background Patients with Marfan Syndrome and related disorders have abnormal wall properties throughout the thoracic aorta including low distensibility in areas that eventually dilate. CFD modeling based on MRI data can be used to quantify distensibility and indices such as velocity and wall shear stress (WSS) throughout the cardiac cycle and for the entire thoracic aorta. We sought to use card...

Fourteen patients with Marfan syndrome, defined according to present criteria, had bone mineral content of the distal forearm measured by single photon absorptiometry. Patients were matched for age and sex with a large local group of healthy volunteers. While further work is needed with other methods of densitometry with measurements at other sites, our results provide no evidence that there is...