نتایج جستجو برای: neuroaxonal dystrophy

تعداد نتایج: 22776  

2017
Frederike C. Oertel Hanna Zimmermann Janine Mikolajczak Maria Weinhold Ella Maria Kadas Timm Oberwahrenbrock Florence Pache Judith Bellmann-Strobl Klemens Ruprecht Friedemann Paul Alexander U. Brandt

Neuromyelitis optica spectrum disorders (NMOSDs) are relapsing inflammatory demyelinating disorders with optic neuritis (ON) as the hallmark. ON causes neuroaxonal damage to the optic nerve and retina, regularly leading to severely impaired visual acuity (VA). Peripapillary retinal nerve fiber layer (pRNFL) thickness measured by optical coherence tomography (OCT) has been increasingly recognize...

Journal: :Magnetic resonance in medicine 2001
T Watanabe T Michaelis J Frahm

This study describes the neuroaxonal tracing of the visual pathway in the living rat using high-resolution T1-weighted 3D gradient-echo MRI (195 x 195 x 125 microm3) at 8, 24, 48, and 72 h after intraocular Mn2+ injection (0.1 microl of 1 M aqueous MnCl2). Best results were obtained at 24 h postinjection, revealing a continuous pattern of anterograde labeling from the retina, optic nerve, and c...

Journal: :iranian journal of child neurology 0
mohammad barzegar 1. pediatric health research center, tabriz university of medical sciences, tabriz, iran. 2. division of pediatric neurology, tabriz children’s hospital, tabriz university of medical sciences, tabriz, iran parinaz habibi 1. pediatric health research center, tabriz university of medical sciences, tabriz, iran. mortaza mortaza bonyady 3. center of excellence for biodiversity, department of molecular medical genetics, faculty of natural sciences university of tabriz, tabriz, iran vahideh topchizadeh 4. physical medicine & rehabilitation research center, tabriz university of medical sciences, tabriz, iran shadi shiva* 1. pediatric health research center, tabriz university of medical sciences, tabriz, iran. 2. division of pediatric neurology, tabriz children’s hospital, tabriz university of medical sciences, tabriz, iran

how to cite this article: barzegar m, habibi p, bonyady m, topchizadeh v, shiva sh. exon deletion pattern in duchene muscular dystrophy in north west of iran. iran j child neurol. 2015 winter; 9(1): 42-48. abstract objective duchene and becker muscular dystrophy (dmd/ bmd) are x-linked disorders that both are the result of heterogeneous mutations in the dystrophin gene. the frequency and distri...

Journal: :genetics in the 3rd millennium 0
غلامرضا زمانی gholamreza zamani child neurologist, children's medical center, tehran university of medical sciences (tums)

muscular dystrophies are inherited disorders that cause progressive muscle weakness (myopathy) and atrophy (loss of muscle mass) due to defects in one or more genes required for normal muscle function. some of the genes responsible for these conditions have been identified .there are a number of different types of muscular dystrophy. the primary symptom for most types is muscle weakness, althou...

Journal: :Journal of Veterinary Diagnostic Investigation 1995

Journal: :Cell 2011
Wei Liu Wenyu Wen Zhiyi Wei Jiang Yu Fei Ye Che-Hsiung Liu Roger C. Hardie Mingjie Zhang

INAD is a scaffolding protein that regulates signaling in Drosophila photoreceptors. One of its PDZ domains, PDZ5, cycles between reduced and oxidized forms in response to light, but it is unclear how light affects its redox potential. Through biochemical and structural studies, we show that the redox potential of PDZ5 is allosterically regulated by its interaction with another INAD domain, PDZ...

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