A congenital absence of the portal vein (CAPV) is a rare disorder that may lead to an intrapulmonary shunt. A 14-year-old male with CAPV underwent living donor liver transplantation with a left lobe graft from his father. The portal vein reconstruction was achieved with a renoportal anastomosis using an interpositional graft from the native collateral vein, because portal venous system directly...

A transjugular intrahepatic portal-systemic shunt (TIPS) is a standard way to decompress the portal system in cirrhotic patients as a bridge to orthotopic liver transplantation (OLT). Traditionally, TIPS has been indicated for certain portal hypertensive sequelae such as refractory ascites, varices treatment and even hepato-hydrothorax. Herein is a case report on the efficacy of TIPS in an OLT ...

quired as a result of trauma, including a liver biopsy, or in association with hepatic tumors and ruptured aneurysms of the hepatic artery (1). A congenital hepatoportal arteriovenous fistula is extremely rare and there are very few reports. The common clinical manifestations are the features of portal hypertension such as bowel congestion, gastrointestinal bleeding, malabsorption, ascites and ...

The long-term prognosis in congenital hepatic fibrosis has been assessed in 30 patients, 13 treated at Newcastle and 17 from other British centres. Twenty-four patients had been followed-up for more than five years from diagnosis. Shunt operations, performed in 18 patients, were successful in controlling haemorrhage with a low mortality (1/18), low incidence of recurrent haemorrhage (3/18) and ...

Multiple intrahepatic portosystemic shunt (IPSS) without portal hypertension, now thought to be congenital in origin, is very rare. The presence of IPSS, unlike other congenital diseases, may not be recognized for several decades due to the time it takes to develop hepatic encephalopathy. In this article, we report an autopsy case of an 80-year-old Japanese woman with a one-month history of hyp...

Despite advances in cardiovascular medicine, the endogenous mechanisms responsible for positive inotropic state of the heart is poorly understood. We have assessed surgical transposition of the portal vein (portacaval shunt) as a procedure providing total systemic delivery of portal venous effluent in six dogs. The animals recovered rapidly from the surgery maintaining euglycemia. Four days aft...