Abstract Background Primitive neuroectodermal tumor commonly occurs in bones and is equivalent to Ewing’s sarcoma. Very few cases have been reported the literature they had a very different presentation aggressive behavior. Case We present case of young 23-year-old male who presented with complaints pain left lumbar region abdomen since 8 months hematuria off on. CT scan was done which revealed...

RATIONALE Peripheral primitive neuroectodermal tumor (PNET) is a kind of small round cell tumor derived from primitive neuroectodermal tumor. PATIENT CONCERNS PNET is a highly malignant tumor that is subordinated to Ewing sarcoma. It occurs predominantly in soft tissue and bone and rarely in the bronchi and lung. Traditional surgery, radiotherapy, and chemotherapy are used for the treatment o...