Sixty-two patients with tricuspid atresia admitted for cardiac catheterisation between 1967 and 1974 have been classified according to the anatomical and radiological findings into those with normally related great arteries (type I: 39 cases) and those with transposition of the great arteries (type II: 23 cases). These types were further subdivided into group A (reduced lung vascularity),groupB...

Pulmonary torsion is a severe, life-threatening event, rarely occurring in children. We present a case of atypical postoperative complication of esophageal atresia repair in the form of pulmonary torsion comprising the middle lobe of the right lung. Clinical deterioration in the face of normal arterial blood gases should rise a high index of suspicion for pulmonary torsion. Early diagnosis is c...

The systemic to pulmonary artery shunts are done as palliative procedures for cyanotic congenital heart diseases ranging from simple tetralogy of Fallots (TOFs)/pulmonary atresia (PA) to complex univentricular hearts. They allow growth of pulmonary arteries and maintain regulated blood flow to the lungs till a proper age and body weight suitable for definitive corrective repair is reached. We h...

We report on a premature neonate who presented with cyanosis soon after birth. She was found on echocardiography to have an unguarded tricuspid valve orifice associated with pulmonary valve atresia and an intact interventricular septum. Owing to the small-sized pulmonary arteries, she was initially managed conservatively with prostaglandin infusion, and at one year of age underwent a successful...

OBJECTIVE Correlate the anatomic features of atrioventricular septal defect with echocardiographic images. MATERIALS AND METHODS Sixty specimen hearts were studied by sequential segmental analysis. Echocardiograms were performed on 34 patients. Specimen hearts with findings equivalent to those of echocardiographic images were selected in order to establish an anatomo-echocardiographic correla...

To cite: Mathew JJ, Hollings NP, Myers JD. Thorax 2013;68:796–797. An 18-year-old female subject with a history of decortication for right sided, postpneumonic pleural thickening presented with haemoptysis. A CT pulmonary angiogram showed marked hypoplasia of the right main, lobar and segmental pulmonary arteries, along with reduced volume of the right lung. Prominent bronchial artery supply to...

Most cases of pulmonary atresia have the general anatomical features of Fallot's tetralogy with atresia at or near the pulmonary valve instead of stenosis, but in one quarter of the necropsy cases the ventricular septum is intact instead of having a defect (24%, Peacock, 1866, and Abbott, 1936). The general features, based on six cases with necropsy, have been discussed by Allanby et al. (1950)...

Neonates with pulmonary atresia and intact interventricular septum (PAIVS) do not have pulmonary vascular disease secondary to their heart abnormality. Persistent pulmonary hypertension of the newborn has not been described in association with this condition. The case is reported of a female neonate born with PAIVS, who preoperatively had no clinical evidence or any risk factors for persistent ...