Introduction Spontaneous pneumothorax usually occurs sporadically in healthy young adults and the cause is often unknown. Kjaergaard (1935), and Brock (1948) favoured the presence of hereditary congenital lung cysts, which by rupturing, produced a pneumothorax. Familial cases of spontaneous pneumothorax have been described several times since the original description by Faber (1921). The occurr...