نتایج جستجو برای: systemic sclerosis ssc

تعداد نتایج: 234343  

2016
Katarzyna Romanowska-Próchnicka Marcela Walczyk Marzena Olesińska

Systemic sclerosis is a complex disease characterized by autoimmunity, vasculopathy and tissue fibrosis. Although most patients present with some degree of skin sclerosis, which is a distinguishing hallmark, the clinical presentation vary greatly complicating the diagnosis. In this regard, new classification criteria were jointly published in 2013 by American College of Rheumatology (ACR) and E...

2016
Tracy M. Frech Kathleen Boynton Erinn Downs-Kelly Bryan Jones John D. Kriesel Kathryn Peterson

The gastrointestinal tract (GIT) is the most common extracutaneous organ system damaged in systemic sclerosis (SSc) and is the presenting feature in 10% of patients. The esophagus as the portion of the GIT is the most commonly affected and there is an association of gastroesophageal reflux (GER) with SSc interstitial lung disease (ILD). Thus, an aggressive treatment for GER is recommended in al...

2015
Nobuhiro Kanaji Masaya Okuda Hiroaki Dobashi Tomohiro Kameda Akira Tadokoro Risa Wakiya Norimitsu Kadowaki Shuji Bandoh

We here describe a 50-year-old woman diagnosed with squamous cell lung cancer (SqLC) with underlying interstitial lung disease (ILD) 14 years after a diagnosis of systemic sclerosis (SSc). We reviewed the literature and collected 21 well-documented cases with SqLC associated with SSc including the present case. Several characteristics of SqLC associated with SSc have been found. First, the aver...

Journal: :Clinical and experimental rheumatology 2001
G Kumánovics H Zibotics E Juhász A Komócsi L Czirják

OBJECTIVE To assess the presence of neutrophil and lymphocyte fibrosing alveolitis by bronchoalveolar lavage in patients with early undifferentiated connective tissue disease (EUCTD) and systemic sclerosis (SSc). METHOD Bronchoalveolar lavage (BAL) was performed in 13 patients with EUCTD who exhibited signs of lung involvement by non-invasive methods including lung function tests and high res...

Journal: :The European respiratory journal 2012
Hanadi Dib Mathieu C Tamby Guillaume Bussone Alexis Regent Alice Berezné Claudine Lafine Cédric Broussard Gérald Simonneau Loïc Guillevin Véronique Witko-Sarsat Marc Humbert Luc Mouthon

Anti-endothelial cell antibodies (AECAs) have been identified in patients with systemic sclerosis (SSc) with and without pulmonary arterial hypertension (PAH) and in patients with idiopathic pulmonary arterial hypertension (iPAH). However, their target antigens remain poorly identified. Sera from 24 patients with SSc without PAH, 20 patients with SSc with PAH, 30 with iPAH and 12 healthy contro...

2015
Pia Moinzadeh Elisabeth Aberer Keihan Ahmadi-Simab Norbert Blank Joerg H W Distler Gerhard Fierlbeck Ekkehard Genth Claudia Guenther Ruediger Hein Joerg Henes Lena Herich Ilka Herrgott Ina Koetter Alexander Kreuter Thomas Krieg Kathrin Kuhr Hanns-Martin Lorenz Florian Meier Inga Melchers Hartwig Mensing Ulf Mueller-Ladner Christiane Pfeiffer Gabriela Riemekasten Miklós Sárdy Marc Schmalzing Cord Sunderkoetter Laura Susok Ingo H Tarner Peter Vaith Margitta Worm Gottfried Wozel Gabriele Zeidler Nicolas Hunzelmann Nil Mona Ahrazoglu Mike Oliver Becker Rudolf Mierau Gunther Neeck Christoph Fiehn Aaron Juche Andrea Rubbert Manfred Weber Rebecca Fischer-Betz Michael Sticherling Harald Burkhardt Michaela Koehm Cornelia S Seitz Claudia Herink Ivan Foeldvári Johannes Norgauer Dieter Schoeffel Regina Renner Mirjana Ziemer Kerstin Steinbrink Rudolf Stadler Verena Müller Mahzad Ziai Sigrid Karrer Michael Landthaler Rotraud Meyringer Michael Buslau Dirk Tomsitz Hae- Hyuk Lee Percy Lehmann Noemi Gaebelein-Wissing Marieke Wagner Joachim Ebel Christian Beyer Rita Varga Agnes Bretterklieber Frank Reichenberger Andrea Himsel

BACKGROUND Systemic sclerosis (SSc)-overlap syndromes are a very heterogeneous and remarkable subgroup of SSc-patients, who present at least two connective tissue diseases (CTD) at the same time, usually with a specific autoantibody status. OBJECTIVES To determine whether patients, classified as overlap syndromes, show a disease course different from patients with limited SSc (lcSSc) or diffu...

2017
Bin Zhou Xiao Xia Zuo Yi Sha Li Si Ming Gao Xiao Dan Dai Hong Lin Zhu Hui Luo

MicroRNAs (miRNAs) play important roles in the fibrosis of systemic sclerosis (SSc). However, the underlying miRNA-mRNA regulatory network is not fully understood. A systemic investigation of the role of miRNAs would be very valuable for increasing our knowledge of the pathogenesis of SSc. Here, we combined miRNA and mRNA expression profiles and bioinformatics analyses and then performed valida...

Journal: :Revista brasileira de reumatologia 2011
Carolina de Souza Müller Eduardo Dos Santos Paiva Valderílio Feijó Azevedo Sebastião Cezar Radominski José Hermênio Cavalcante Lima Filho

OBJECTIVES To assess the manifestations of systemic sclerosis (SSc), with an emphasis on the analysis of autoantibodies and their clinical correlations, in a population of patients followed up at the SSc Outpatient Clinics of the Hospital de Clínicas of the Universidade Federal do Paraná. METHODOLOGY Cross-sectional study with 96 patients followed up at the SSc Outpatient Clinics of the hospi...

2014
Shinji Noda Yoshihide Asano Satoshi Nishimura Takashi Taniguchi Katsuhito Fujiu Ichiro Manabe Kouki Nakamura Takashi Yamashita Ryosuke Saigusa Kaname Akamata Takehiro Takahashi Yohei Ichimura Tetsuo Toyama Daisuke Tsuruta Maria Trojanowska Ryozo Nagai Shinichi Sato

Systemic sclerosis (SSc) is manifested by fibrosis, vasculopathy and immune dysregulation. So far, a unifying hypothesis underpinning these pathological events remains unknown. Given that SSc is a multifactorial disease caused by both genetic and environmental factors, we focus on the two transcription factors, which modulate the fibrotic reaction and are epigenetically suppressed in SSc dermal...

2015
Benjamin D. Korman Lindsey A. Criswell

Significant advances have been made in understanding the genetic basis of systemic sclerosis (SSc) in recent years. Genomewide association and other large-scale genetic studies have identified 30 largely immunity-related genes which are significantly associated with SSc. We review these studies, along with genomewide expression studies, proteomic studies, genetic mouse models, and insights from...

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