Congenital absence of an internal carotid artery is a rare anomaly. Less than 1 00 cases have been reported in the English literature. It is usually associated with collateral flow to the involved vascular territory, so neurologic deficits are few. However, this anomaly is also associated with a high occurrence of intracranial aneurysms. We report two cases of absent internal carotid artery wit...

BACKGROUND Internal carotid artery agenesis is a rare anomaly that can be clinically asymptomatic. Klippel-Feil syndrome is a skeletal malformation characterized by vertebral fusion. Presence of postaxial polydactyly is suggestive of an underlying syndrome. CASE REPORT We report a rare case of a 44-year-old patient with non-specific symptoms and an association between these three rare abnorma...

KILT syndrome is a rare condition composing the triad of kidney and inferior vena cava anomaly and extensive venous thrombosis. We present a case of newly diagnosed KILT syndrome in a 41-years-old gentleman presenting with loin pain and fever. Reviewing previous case reports, KILT syndrome is usually an incidental finding on imaging studies and there is a wide scope of initial clinical presenta...

BACKGROUND Superficial ulnar artery is a well-known vascular anomaly that may cause special risks because of possible impairment of the vessel by mistake during harvesting fasciocutaneous forearm flaps. METHODS The charts of patients who had undergone forearm flap transfer were reviewed for vascular anomalies. When a superficial ulnar artery was present, a superficial ulnar artery flap was ra...

OBJECTIVE Disc edge veins of Kraupa are a rare anomaly of the retinal venous system in which the main trunk of the retinal vein disappeared into the margin of the optic disc instead of its centre. METHODS A 40-year-old woman was detected to have an anomaly in her left optic disc in a routine eye examination. The eyes had an anomaly of the retinal venous system in which all branches of the ret...

Infraoptic anterior cerebral artery (ACA) is an extremely rare congenital anomaly. This anomalous artery usually arises from the intradural internal carotid artery (ICA) near the level of the ophthalmic artery (OA) or rarely from the extradural ICA. This anomaly frequently harbors a cerebral aneurysm, and may involve other coexisting vascular anomalies. In the case of this anomaly, surgical tre...

Right aortic arch is a rare congenital vascular anomaly, thus, the surgical resection of esophageal cancer in a patient with this anomaly is extremely uncommon. The surgical treatment of esophageal cancer was performed in a 73-year-old man with right aortic arch. An upper GI series and endoscopy revealed Type 2 esophageal cancer in the lower thoracic esophagus. Chest computed tomography reveale...

PURPOSE To investigate the value of prospective ECG-gated high-pitch 128-slice dual-source CT (DSCT) angiography in the diagnosis of congenital extracardiac vascular anomalies in infants and children in comparison with transthoracic echocardiography (TTE). METHODS Eighty consecutive infants or children clinically diagnosed of congenital heart disease and suspected with extracardiac vascular a...

Vascular anomalies are classified into vascular tumors and vascular malformations based on the classification system of the International Society for the Study of Vascular Anomalies (ISSVA). Vascular tumors are characterized by proliferation and tumor enlargement, and the most common vascular tumor is infantile hemangioma, while a less common vascular tumor is hemangiopericytoma. Vascular malfo...

Persistent left superior vena cava is rare but important congenital vascular anomaly. It results when the left superior cardinal vein caudal to the innominate vein fails to regress. It is most commonly observed in isolation but can be associated with other cardiovascular abnormalities including atrial septal defect, bicuspid aortic valve, coarctation of aorta, coronary sinus ostial atresia, and...