نتایج جستجو برای: wilms tumor gene 1

تعداد نتایج: 3825016  

2014
Sandra Hanks Elizabeth R. Perdeaux Sheila Seal Elise Ruark Shazia S. Mahamdallie Anne Murray Emma Ramsay Silvana Del Vecchio Duarte Anna Zachariou Bianca de Souza Margaret Warren-Perry Anna Elliott Alan Davidson Helen Price Charles Stiller Kathy Pritchard-Jones Nazneen Rahman

Wilms tumour is a childhood kidney cancer. Here we identify inactivating CTR9 mutations in 3 of 35 Wilms tumour families, through exome and Sanger sequencing. By contrast, no similar mutations are present in 1,000 population controls (P<0.0001). Each mutation segregates with Wilms tumour in the family and a second mutational event is present in available tumours. CTR9 is a key component of the ...

Journal: :Medical and pediatric oncology 2003
Herwig Lackner Christian Urban Hans Jürgen Dornbusch Wolfgang Schwinger Reinhold Kerbl Petra Sovinz

1. Webber BL, Parham DM, Drake LG, et al. Renal tumors in childhood. Pathol Ann Part 1992;1:191–232. 2. Murphy WM, Beckwith JB, Farrow GM. Tumors of the kidney, bladder and related urinary structures. In: Murphy WM, Beckwith JB, Farrow GM, editors. Atlas of tumor pathology, series 3, fascicle 11. Washington D.C.: Armed Forces Institute of Pathology, 1994. 3. Beckwith JB. Pediatric neoplastic di...

2006
Seon Park Gail Tomlinson Perry Nisen Daniel A. Haber

WAGR syndrome is an acronym for a rare constellation of congenital abnormalities including predisposition to Wilms' tumor, Aniridia, Geni tourinary malformations, and mental Retardation. These congenital de fects are associated with a constitutional deletion affecting one copy of chromosome band Ilpl3, implicating the loss of one alÃ-elefrom a number of contiguous genes in this syndrome. Predis...

2013
Samuel P. Carmichael Joseph F. Pulliam John A. D'Orazio

We describe the case of a 5-year-old girl whose abdominal pain and distension were caused by Wilms tumor of the kidney. Because of the bilateral nature of her disease, she was spared biopsy or initial nephrectomy as part of her treatment course. Rather, she was treated presumptively for Wilms tumor based primarily on radiologic findings. Neoadjuvant chemotherapy consisting of vincristine, dacti...

2011
Ayse Elif Erson Elizabeth M Petty

Other names: Nephroblastoma Note: Wilms' tumor, although generally rare, is the most common abdominal malignancy in children. Wilms' tumor cells are believed to derive from pluripotent embyronic renal precursor cells. Thus, Wilms' tumors are linked to the early development of the kidney. While most are isolated sporadic tumors, approximately 10% of cases are associated with genetic syndromes an...

Journal: :Revista Ciencia y Salud Integrando Conocimientos 2020

Journal: :Journal of the Chinese Medical Association : JCMA 2004
Be-Fong Chen Chin-yuen Tzen Der-Cherng Liang Hsi-Che Liu Yu-Wen Huang Chi-Chen Fan

BACKGROUND Approximately 10% of nephroblastomas (Wilms' tumors) carry mutations in the Wilms' tumor 1 (WT1) gene. Recently, a WT1 antibody raised against N-terminal 1-181 amino acids of human WT1 became commercially available for immunohistochemical use on paraffin-embedded tissue. The aim of this study was to investigate the diagnostic and prognostic value of WT1 N-terminal antibody in nephrob...

Journal: :Cancer research 1993
E Austruy M Cohen-Salmon C Antignac C Béroud I Henry V C Nguyen L Brugières C Junien C Jeanpierre

We applied a subtractive hybridization approach to isolate genes differentially expressed between mature kidney and Wilms' tumor. We constructed a complementary DNA library from a total mature kidney complementary DNA subtracted by an excess of mRNA from a Wilms' tumor, WAGR4, with a germline deletion of 11p13 and a somatic loss of alleles at 11p15. Six clones presenting a differential pattern ...

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