نتایج جستجو برای: acid ceramidase

تعداد نتایج: 747667  

2017
Chih-Li Lin Ruijuan Xu Jae Kyo Yi Fang Li Jiang Chen Evan C. Jones Jordan B. Slutsky Liqun Huang Basil Rigas Jian Cao Xiaoming Zhong Ashley J. Snider Lina M. Obeid Yusuf A. Hannun Cungui Mao

Ceramides and their metabolites are important for the homeostasis of the epidermis, but much remains unknown about the roles of specific pathways of ceramide metabolism in skin biology. With a mouse model deficient in the alkaline ceramidase (Acer1) gene, we demonstrate that ACER1 plays a key role in the homeostasis of the epidermis and its appendages by controlling the metabolism of ceramides....

2012
Nobutomo Ikarashi Wataru Sato Takahiro Toda Makoto Ishii Wataru Ochiai Kiyoshi Sugiyama

We examined the inhibitory effect of polyphenol-rich aqueous extract from the bark of Acacia mearnsii (PrA) on itching associated with atopic dermatitis (AD). HR-1 mice were fed a normal diet, special diet (AD group), or special diet containing 3% PrA (PrA group) for 6 weeks. In the AD group, itching frequency and transepidermal water loss increased compared to the control group. In the PrA gro...

Journal: :The Biochemical journal 2003
Hatsumi Monjusho Nozomu Okino Motohiro Tani Mineko Maeda Motonobu Yoshida Makoto Ito

The nucleotide sequence reported for the Dictyostelium discoideum ceramidase is available on the DNA Data Bank of Japan (DDBJ). Ceramidases (CDases) are currently classified into three categories (acid, neutral and alkaline) based on their optimal pHs and primary structures. Here, we report the first exception to this rule. We cloned the CDase cDNA, consisting of 2142 nucleotides encoding 714 a...

Journal: :Nature chemical biology 2015
Tomas Blom Shiqian Li Andrea Dichlberger Nils Bäck Young Ah Kim Ursula Loizides-Mangold Howard Riezman Robert Bittman Elina Ikonen

Lysosome-associated protein transmembrane-4b (LAPTM4B) associates with poor prognosis in several cancers, but its physiological function is not well understood. Here we use novel ceramide probes to provide evidence that LAPTM4B interacts with ceramide and facilitates its removal from late endosomal organelles (LEs). This lowers LE ceramide in parallel with and independent of acid ceramidase-dep...

2014
Alexander Sólyom Nesrin Karabul Boris Hügle Calogera Simonaro Edward Schuchman

Introduction Farber lipogranulomatosis (Farber Disease; FD) is an ultra-rare lysosomal storage disorder resulting from the inherited deficiency of the enzyme acid ceramidase, and the accumulation of the lipid substrate, ceramide. Ceramide is a pro-inflammatory and pro-apoptotic lipid that has been implicated in the pathogenesis of cartilage disorders. Farber Disease has a heterogeneous presenta...

2017
Heike Grassmé Brian Henry Regan Ziobro Katrin Anne Becker Joachim Riethmüller Aaron Gardner Aaron P. Seitz Joerg Steinmann Stephan Lang Christopher Ward Edward H. Schuchman Charles C. Caldwell Markus Kamler Michael J. Edwards Malcolm Brodlie Erich Gulbins

Chronic pulmonary colonization with bacterial pathogens, particularly Pseudomonas aeruginosa, is the primary cause of morbidity and mortality in patients with cystic fibrosis (CF). We observed that β1-integrins accumulate on the luminal membrane of upper-airway epithelial cells from mice and humans with CF. β1-integrin accumulation is due to increased ceramide and the formation of ceramide plat...

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