نتایج جستجو برای: antibody deficiency syndrome

تعداد نتایج: 889912  

2013
Jaspreet Khangura Ann Van den Bruel Rafael Perera Carl Heneghan Christopher P Price Jane Wolstenholme Matthew Thompson Annette Plüddemann

British Journal of General Practice, June 2013 e426 BaCkground and advantages over exIstIng teChnology Coeliac disease is a malabsorption syndrome precipitated by gluten ingestion, and characterised by inflammation of the small intestine. Serological tests for IgA anti-tissue transglutaminase antibody (tTGA) and anti-endomysial antibody (EMA) have high sensitivity and specificity for coeliac di...

Journal: :Clinical immunology 2012
Xiying Fan Bhaskar Upadhyaya Liming Wu Christopher Koh Mónica Santín-Durán Stefania Pittaluga Gulbu Uzel David Kleiner Ester Williams Chi A Ma Aaron Bodansky Joao B Oliveira Pamela Edmonds Ronald Hornung Duane W Wong Ronald Fayer Tom Fleisher Theo Heller Calman Prussin Ashish Jain

X-linked hyper-IgM syndrome (XHM) is a combined immune deficiency disorder caused by mutations in CD40 ligand. We tested CP-870,893, a human CD40 agonist monoclonal antibody, in the treatment of two XHM patients with biliary Cryptosporidiosis. CP-870,893 activated B cells and APCs in vitro, restoring class switch recombination in XHM B cells and inducing cytokine secretion by monocytes. CP-870,...

A MOHEBBI, F NOOHI, HA BASSIRI, V SINEH SEPEHR,

A 31 year old woman was hospitalized for evaluation of aortic valve insufficiency and her present cardiac status. Clinical and paraclinical findings strongly suggested the presence of a collagen vascular inflammatory processprecisely, the antiphospholipid antibody syndrome (APS), with systemic lupus erythematosus as the underlying disease.

2012
Ricardo U. Sorensen Tammy Harvey Lily E. Leiva

Specific antibody deficiency (SAD) is a common antibody immunodeficiency defined as a poor antibody response to unconjugated pneumococcal polysccharides present in the 23valent pneumococcal vaccine (PPV23). Clinical manifestations of specific antibody deficiency include recurrent sinopulmonary infections, such as sinusitis, otitis media, bronchitis, and pneumonia. All immunoglobulin concentrati...

Journal: :Archives of Disease in Childhood 1989

Journal: :Journal of the American Society of Nephrology : JASN 2005
Marie-Agnès Dragon-Durey Chantal Loirat Sylvie Cloarec Marie-Alice Macher Jacques Blouin Hubert Nivet Laurence Weiss Wolf Herman Fridman Véronique Frémeaux-Bacchi

Several studies have demonstrated genetic predisposition in non-shigatoxin-associated hemolytic uremic syndrome (HUS), involving regulatory proteins of the complement alternative pathway: Factor H (FH) and membrane co-factor protein (CD46). Regarding the observations of thrombotic thrombocytopenic purpura patients, in whom a von Willebrand factor protease (ADAMST-13) deficiency may be inherited...

Akbar Rajaee Elham Aflaki Mohammad Ali Nazarinia Zahra Habibagahi,

Background: The clinical significance of antiphospholipid antibodies in patients with chronic hepatitis C virus (HCV) and some other viral infections is controversial. Objective: To study the prevalence of anticardiolipin antibody (ACLA) and antibeta2glycoproteinI antibody (antibeta2GPI antibody) in HCV and hepatitis B virus (HBV) infected patients and its association with liver clinical parame...

2017
Johanna Schepp Janet Chou Andrea Skrabl-Baumgartner Peter D. Arkwright Karin R. Engelhardt Sophie Hambleton Tomohiro Morio Ekkehard Röther Klaus Warnatz Raif Geha Bodo Grimbacher

BACKGROUND Inducible co-stimulator (ICOS) deficiency was the first monogenic defect reported to cause common variable immunodeficiency (CVID)-like disease in 2003. Since then, 16 patients have been reported worldwide with an increasing range of clinical phenotypes. OBJECTIVE We sought to compare the clinical and immunological phenotype and provide clinical follow-up and therapeutic approaches...

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