Background Behcet’s disease (BD) is an auto-inflammatory disorder, characterized by recurrent aphthous stomatitis, genital ulcers, uveitis, erythema nodosum and other numerous mucocutaneous, gastrointestinal, neurological, vascular manifestations. Despite many biomarkers (anti-lysozyme, serum endocan, alpha 1-acid glycoprotein (AGP)) have been investigated for evaluating activity predicting sev...

A 78 year old man with a history of hypertension, arteriosclerosis, and a myocardial infarction woke up one morning to realise that he had lost his voice. He did not feel ill nor had he experienced symptoms of cough or fever. He had smoked cigarettes for over 60 years and had a brother with lung cancer. Left vocal cord paralysis was assessed at laryngoscopy. A contrast enhanced computed tomogra...

Giant serpentine aneurysms are uncommon types of aneurysmal disease and have angiographically authentic features. We report a case of a 44-year-old male with headache and seizure. He presented a giant serpentine aneurysm arising from the middle cerebral artery (MCA). It was a large intracranial aneurysm thrombosed as a mass-like lesion while it maintained its outflow drainage into the distal MC...

INTRODUCTION Vasculo-Behcet's disease is a subtype of Behcet's disease, characterized by cases in which vascular complications are present and often dominate the clinical features. In this disease, there are four different vascular complications: arterial occlusion, arterial aneurysm or pseudoaneurysm, venous thrombosis, and variceal formation. It is rare that arterial lesions are multiple, but...

Behçet's disease is a vasculitic disorder in which the aetiopathogenetic pathway has not yet been clarified. Many organs and systems may be affected in BD. The causes of the wide-ranged clinical spectrum and the variable severity of involvement, including the kidneys remain to be defined. Behçet's disease should also be considered in the differential diagnosis of AA amyloidosis as well as vascu...

Dear Sir, We describe a patient with progressive locked-in syndrome due to a giant interpeduncular basilar aneurysm that initially underwent coiling and eventually clipping. The case is unusual because the locked-in syndrome was caused by severe midbrain compression rather than an ischemic infarction of the basis pontis, had a gradual rather than abrupt onset and was accompanied by vertical rat...

Spinal cord ischemia is an uncommon complication of an abdominal aortic aneurysm (AAA). We report the case of a 59-year-old man admitted for an acute ischemic Cauda equina syndrome secondary to a spinal cord embolization from an unknown partially thrombosed aortic aneurysm. The patient being at risk of further embolization, we achieved an emergency EVAR. The vascular post-operative course was u...

Hughes-Stovin syndrome (HSS) is a rare clinical disorder, which has been described as the presence of pulmonary artery aneurysm in the setting of systemic thrombosis. The term "Incomplete Behçet's Disease" has also been used to describe this syndrome due to the clinical and histopathological similarities between Behçet's disease and HSS. Indeed, pulmonary involvement can be indistinguishable be...

A case of neurofibromatosis type 1 (NF1) manifesting Wallenberg's syndrome and fusiform aneurysm of the basilar artery is reported. The patient suddenly developed dysarthria, walking difficulty and sensory disturbance. Neurological examination suggested Wallenberg's syndrome and MR imaging confirmed an ischemic lesion at the left lateral medulla oblongata. Cerebral angiography revealed a fusifo...

We report a 13-year-old girl with Loeys-Dietz syndrome (LDS) caused by a known transforming growth factor beta receptor II (TGFBR2) gene mutation, who developed aortic root dilatation and saccular aneurysm of the internal carotid artery. LDS is a rare, autosomal dominant aortic aneurysm syndrome with multisystem involvement. The disease is typically characterized by the triad of arterial tortuo...