The importance of identifying this anomaly is that it is associated with other congenital malformations in over 20% of cases, most commonly being associated with cardiovascular anomalies and congenital dislocation of hip. Of the 44 infants with this syndrome, Pape and Pickering found 27 to have major anomaly of skeletal, genitourinary, respiratory and cardiovascular systems. The disorder most c...

A case is reported of herniation of the left atrial appendage through a partial pericardial defect, probably congenital. The diagnosis was suggested by the history of chest pain and bulging of the middle segment of the left heart border on the plain chest film, without other signs. Angiography revealed a dilated left atrial appendage. An artificial left pneumothorax confirmed the presence of a ...

background pulmonary artery banding (pab) is a technique of palliative surgical therapy used by congenital heart surgeons as a staged approach to operative correction of congenital heart defects. materials and methods we report 5- year experiences from january 2011 to january 2016 of imam reza hospital center (a tertiary referral hospital in mashhad city, north east of iran) that consist of 50 ...

discussion children with congenital heart disease are at risk of acquiring gram-negative endocarditis even if they have not had other predisposing factors. case presentation in this study a ten-year-old boy with ventricular septal defect, who was not immune compromised and acquired klebsiella endocarditis is introduced. the patient had a favorable response to medical treatment and underwent a s...

Congenital heart disease is the most common congenital defect. During childhood, survival is generally good but, in adulthood, late complications are not uncommon. Abnormal autonomic control in children with congenital heart disease may contribute considerably to the pathophysiology of these long term sequelae. This narrative review of 34 studies aims to summarize current knowledge on function ...

The ventricular septal defect is the most common congenital cardiac defects in sheep, cattle and horses. It occurs frequently as a subaortic defect. Echocardiography is a rapid and noninvasive method for evaluation of cardiac congenital disease in animals. This diagnostic technique that can provide a wealth of helpful information including the size and shape of the heart, its pumping strength a...

AIMS Pulmonary hypertension (PH) in asymptomatic patients is a rare cause of sudden death. This study aims to determine the incidence of this entity and raise awareness among pathologists. METHODS We retrospectively investigated 44 cases of sudden unexpected death in relation to PH in patients not on antihypertensive therapy. This is the largest pathological study reported. RESULTS We repor...

49,xxxxy is rare chromosomal pattern and these patients have mental retardation, small penis, cryptorchidism and skeletal anomalies. we reported a 10 month-old boy who has hypotonia, microcephaly, hypertelorism, depressed nasal bridge, epicanthic folds and bilateral multiple ear tags, high arched palate, down set ears, micrognathia and congenital heart disease such as patent ductus arteriosus (...

normal 0 false false false en-us x-none fa background : fahr's disease is a rare neurodegenerative disorder of unknown cause characterized by idiopathic basal ganglia calcification that is associated with neuropsychiatric and cognitive impairment. no case of fahr's disease with associated cardiac conduction disease has been described in the literature to date. the objective of this case report ...

Background Left-to-right shunting in acyanotic congenital heart disease (CHD) is the most common type of defect childhood disease. Limited access to specialist health services causes delays CHD management. In limited resource settings, identification factors that influence occurrence pulmonary hypertension important order decide which patients should be prioritized for closure prevent further c...