Bu olgu sunumu Hirschsprung Hastalığı’nın nadir görülen bir çeşidi olan Total Kolonik Aganglionozis şüphesi nedeniyle ileostomi açılan bebeğin hemşirelik bakım planının sunulması amacıyla yapılmıştır. Veri toplamada Gordon’un Fonksiyonel Sağlık Örüntüleri Modeli kullanılmıştır. Veriler, hastane bilgi sistem kayıtları, tıbbi tedavi ve hemşire gözlem ebeveynlerle birebir görüşme yöntemi ile topla...

Background: Hirschsprung's disease is the most common cause of pediatric intestinal obstruction. Contrast enema is used for evaluation of the patients with its diagnosis. Aim: To evaluate sensitivity, specificity, positive predictive value, and negative predictive value of radiologic findings for diagnosis of Hirschsprung in patients underwent barium enema. Methods: This cross sectional s...

The neural crest is a transient population of migratory cells in the embryo that gives rise to a wide variety of different cell types, including those of the peripheral nervous system. Dysfunction of neural crest cells (NCCs) is associated with multiple diseases, such as neuroblastoma and Hirschsprung disease. Recent studies have identified NCC behaviors during their migration and differentiati...

Anorectal malformation (ARM) is one of frequent neonatal surgical problem managed in pediatric surgical units. Gastrointestinal malformations are associated in approximately 5% cases of ARM. Some of the common associations are oesophageal atresia and trachea oesophageal fistula, duodenal atresia, hirschsprung`s disease, pouch colon and neuronal intestinal dysplasia [1]. Association of ARM with ...