نتایج جستجو برای: multiplex ligation

تعداد نتایج: 42263  

2012
Anthony Bejjani Mee Rim Choi Linda Cassidy David W. Collins Joan M. O’Brien Tim Murray Bruce R. Ksander Gail M. Seigel

PURPOSE Retinoblastoma (RB), an intraocular tumor of childhood, is commonly associated with mutations in the RB1 gene. RB116 is a novel, early passage RB cell line that has not been previously characterized. In this study, we examined RB116 for the expression of RB1 and tested the hypothesis that RB116 cells would express stem cell markers as well as retinal progenitor cell markers. We compared...

Journal: :BMJ open 2016
Christophe Rosty Mark Clendenning Michael D Walsh Stine V Eriksen Melissa C Southey Ingrid M Winship Finlay A Macrae Alex Boussioutas Nicola K Poplawski Susan Parry Julie Arnold Joanne P Young Graham Casey Robert W Haile Steven Gallinger Loïc Le Marchand Polly A Newcomb John D Potter Melissa DeRycke Noralane M Lindor Stephen N Thibodeau John A Baron Aung Ko Win John L Hopper Mark A Jenkins Daniel D Buchanan

OBJECTIVES Immunohistochemistry for DNA mismatch repair proteins is used to screen for Lynch syndrome in individuals with colorectal carcinoma (CRC). Although solitary loss of PMS2 expression is indicative of carrying a germline mutation in PMS2, previous studies reported MLH1 mutation in some cases. We determined the prevalence of MLH1 germline mutations in a large cohort of individuals with a...

2015
Paulo Marcio Yamaguti Pollyanna Almeida Costa dos Santos Bruno Sakamoto Leal Viviane Brandão Bandeira de Mello Santana Juliana Forte Mazzeu Ana Carolina Acevedo Francisco de Assis Rocha Neves

BACKGROUND Familial hypomagnesemia with hypercalciuria and nephrocalcinosis is a rare autosomal recessive renal disease characterized by tubular disorders at the thick ascending limb of Henle's loop. It is caused by mutations in the tight junction structural proteins claudin-16 or claudin-19, which are encoded by the CLDN16 and CLDN19 genes, respectively. Patients exhibit excessive wasting of c...

2010
Tomás Barato Goucha Jorge Pinto Basto Isabel Alonso

Introduction Neurofibromatosis type 2 is an autosomal dominant disease caused by mutations in the NF2 gene on 22q12.2. Its protein product, merlin, supposedly plays an important role in connecting membrane proteins with the cytoskeleton by coordinating growth-factor signalling. The most common mutations are truncating and splice site mutations, showing a genotype-phenotype correlation. A high r...

Journal: :Cancer research 2006
Jian Zhang Annette Lindroos Saara Ollila Anna Russell Giancarlo Marra Hansjakob Mueller Paivi Peltomaki Martina Plasilova Karl Heinimann

Hereditary nonpolyposis colorectal cancer (HNPCC) is an autosomal dominantly inherited cancer predisposition syndrome caused by germ line mutations in DNA mismatch repair genes, predominantly MLH1 and MSH2, with large genomic rearrangements accounting for 5% to 20% of all mutations. Although crucial to the understanding of cancer initiation, little is known about the second, somatic hit in HNPC...

Journal: :Haematologica 2012
Anna Guarini Marilisa Marinelli Simona Tavolaro Emanuele Bellacchio Monia Magliozzi Sabina Chiaretti Maria Stefania De Propris Nadia Peragine Simona Santangelo Francesca Paoloni Mauro Nanni Ilaria Del Giudice Francesca Romana Mauro Isabella Torrente Robin Foà

BACKGROUND The genetic characterization of chronic lymphocytic leukemia cells correlates with the behavior, progression and response to treatment of the disease. DESIGN AND METHODS Our aim was to investigate the role of ATM gene alterations, their biological consequences and their value in predicting disease progression. The ATM gene was analyzed by denaturing high performance liquid chromato...

Journal: :journal of family and reproductive health 0
hammad ali qazi rtmc, cpsp, karachi, pakistan anjum hashmi prf medical centre, karachi-pakistan

objective: despite development of new contraceptive methods, sterilization remained the most widely used method. our objective was to determine the factors contributing to decision making for tubal ligation in females. materials and methods: a cross sectional study was conducted in jinnah post graduate medical centre (jpmc) between march - november 2008. about 505 females using contraceptive me...

Journal: :Methods in cell biology 2004
Stefan J White Martijn H Breuning Johan T den Dunnen

Using Multiplex Amplifiable Probe Hybridization (MAPH) and Multiplex Ligation-dependent ProbeAmplification (MLPA) we have screened different cohorts of Duchenne/Becker Muscular Dystrophy (DMD/BMD) patients for duplications. In an unselected series the duplication frequency was 8%; in agroup of patients already screened for deletions and point mutations we found a duplication in 64% of<l...

Journal: :Neuro-oncology 2022

Abstract The IDH-wild-type lower-grade astrocytomas are a heterogeneous entity. According to 2021 WHO classification, with any of the following factors show poor prognosis: combination chromosome 7 gain and 10 loss (+7/-10), and/or EGFR amplification, TERT promoter (TERTp) mutation. Multiplex ligation-dependent probe amplification (MLPA) can detect copy number alterations reasonable cost. purpo...

Journal: :European Journal of Medical Genetics 2021

Autosomal dominant polycystic kidney disease (ADPKD) is the most common heritable disease. ADPKD leads to cysts, enlargement and end-stage renal mainly caused by variants in PKD1 PKD2, with truncating causing severe phenotype. This study aimed characterize Danish patients referred for screening of genes related cystic 147 families were analysed PKD1, PKD2 GANAB using next generation sequencing ...

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