نتایج جستجو برای: bilateral wilms

تعداد نتایج: 85842  

Journal: :Atlas of Genetics and Cytogenetics in Oncology and Haematology 2011

Journal: :DMW - Deutsche Medizinische Wochenschrift 1918

2009
Kylie M. Drake E. Cristy Ruteshouser Rachael Natrajan Phyllis Harbor Jenny Wegert Manfred Gessler Kathy Pritchard-Jones Paul Grundy Jeffrey Dome Vicki Huff Chris Jones Micheala A. Aldred

Purpose: Wilms' tumor is a childhood cancer of the kidney with an incidence of ∼1 in 10,000. Cooccurrence of Wilms' tumor with 2q37 deletion syndrome, an uncommon constitutional chromosome abnormality, has been reported previously in three children. Given these are independently rare clinical entities, we hypothesized that 2q37 harbors a tumor suppressor gene important in Wilms' tumor pathogene...

Journal: :Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 2004
Min Hu Geoff Y Zhang Susan Arbuckle Nicole Graf Albert Shun Martin Silink Deborah Lewis Stephen I Alexander

BACKGROUND Denys-Drash syndrome (DDS) is associated with mutations of the Wilms' tumour 1 (WT1) gene, and is characterized by pseudohermaphroditism, a progressive glomerulopathy, and the development of Wilms' tumour. More than 90% of patients with DDS who carry constitutional intragenic WT1 mutations are at high risk (90%) for the development of Wilms' tumour. WT1 is a signalling protein with 9...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2012
Aleksandra Bielen Gary Box Lara Perryman Lynn Bjerke Sergey Popov Yann Jamin Alexa Jury Melanie Valenti Alexis de Haven Brandon Vanessa Martins Vincent Romanet Sebastien Jeay Florence I Raynaud Francesco Hofmann Simon P Robinson Suzanne A Eccles Chris Jones

We have previously demonstrated an increased DNA copy number and expression of IGF1R to be associated with poor outcome in Wilms tumors. We have now tested whether inhibiting this receptor may be a useful therapeutic strategy by using a panel of Wilms tumor cell lines. Both genetic and pharmacological targeting resulted in inhibition of downstream signaling through PI3 and MAP kinases, G(1) cel...

2017
Wen Fu Zhen-Jian Zhuo Wei Jia Jinhong Zhu Shi-Bo Zhu Ze-Feng Lin Feng-Hua Wang Huimin Xia Jing He Guo-Chang Liu

Wilms' tumor is one of the most prevalent pediatric malignancies, ranking fourth in childhood cancer worldwide. TP53 is a critical tumor suppressor gene, which encodes a 53 kDa protein, p53. The p53 functions to protect against cancer by regulating cell cycle and apoptosis and maintaining DNA integrity. TP53 gene is highly polymorphic. Several TP53 gene polymorphisms have been considered to be ...

Journal: :Journal of clinical pathology 1982
H B Marsden W Lawler

The incidence of renal dysplasia in a series of Wilms' tumours is presented. The distribution of such lesions is discussed, together with their course of development and regression. The kidney is regarded as a particularly suitable organ for studying the relation between dysplasia and neoplasia. A schema is suggested for this association with regard to Wilms' tumour.

Journal: :Urologia internationalis 2009
T Maurer C Zorn E Klein G Weirich A J Beer J E Gschwend N Zantl

Wilms tumor, or nephroblastoma, is the most common malignant tumor of the urinary tract in children, but is rarely found in adults. Here, we report the first case of a female patient with a Wilms tumor, diagnosed during pregnancy, who underwent radical nephrectomy and adjuvant chemotherapy before and after delivering a healthy child. Generally, treatment should follow the guidelines established...

2008
Ana Maria Rabelo de Carvalho Luciana Resende Bandeira de Melo Vera Lúcia Moraes Rejane Pereira Neves

Fungal infections are increasingly being reported in immuno-compromised patients. In this study we report a case of systemic Trichosporon cutaneum infection in an infant with Wilms' tumor. This is the first time that an invasive infection for T. cutaneum has been reported in a Wilms' tumor patient.

2009
A. Adil Esen C. Cem Güler Ziya Kirkali

A 64-year-old man underwent left radical nephrectomy for stage III anaplastic Wilms’ tumor. He received adjuvant chemotherapy consisting of cisplatin and etoposide. Complete clinical response was achieved and maintained for 12 months. A systemic relapse after 1 year also responded to three more cycles of cisplatin and etoposide. Although cisplatinand etoposide-based chemotherapy was not used as...

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