rhabdomyosarcoma encompasses a group of malignant myogenic neoplasms expressing a multitude of clinical and pathological diversities. it is the commonest soft tissue sarcoma of childhood but neonates are rarely affected. embryonal subtype is the most frequent. head-neck and genitourinary tracts are predominant sites, while trunk is considered among the unusual sites of rhabdomyosarcoma. herein ...

discussion children with congenital heart disease are at risk of acquiring gram-negative endocarditis even if they have not had other predisposing factors. case presentation in this study a ten-year-old boy with ventricular septal defect, who was not immune compromised and acquired klebsiella endocarditis is introduced. the patient had a favorable response to medical treatment and underwent a s...

conclusions the results of this study indicated that pmv predictors could be specific for each center and a good administration program is needed for each pediatric cardiac surgery center for the preoperative management of patients undergoing congenital heart surgeries. results a total of 300 patients, 56.7% male, were enrolled in this study. their mean age was 32 ± 40 months .the median durati...

introduction : human cytomegalovirus (hcmv) is able to go into latency and is the most common cause of congenital infections in humans. its clinical manifestations range from asymptomatic forms to severe fetal damage, and in rare cases, fetal death due to abortion. this prospective cross-sectional study was designed to determine the seroprevalence of hcmv infection in pregnant women attending a...

supravalvar mitral ring is a rare congenital heart defect of surgical importance. the condition is characterized by an abnormal ridge of the connective tissue on the atrial side of the mitral valve. it often substantially obstructs the mitral valve inflow. we herein introduce a case of a supravalvar mitral ring in a 17-year-old male, who was admitted to our hospital with cardiac syncope. he had...

iniencephaly is a rare kind of neural tube defect that is classified into two types of iniencephaly apertus and iniencephaly clausus. this anomaly could be diagnosed prenatally by obstetric ultrasonography and terminated by therapeutic abortion; however, it could be undiagnosed until birth similar to our case due to the abnormal position of the fetus or lack of experience of the sonographer. du...

nuchal translucency (nt) measurements in the first trimester screening between 11 and 14 weeks’ gestation are regarded as a clear marker for aneuploidies. the presence of a thickened nt, even if the karyotype is normal, can be associated with structural abnormalities. having an abnormal screening of nt, parents and physicians could face dilemma over abortion particularly in a case of ivf/icsi f...

background: hypoalbuminemia may be caused by liver disease, nephrotic syndrome, burns, protein-losing entropathy, malnutrition, and metabolic stress. alterations in albumin in metabolic stress such as cardiac surgery have been previously investigated. we studied serum albumin concentration in children with congenital heart disease and also the association of hypoalbuminemia with mortality and m...

background: coarctation of the aorta (coa) is a defect that accounts for 5-8% of all congenital heart diseases. balloon angioplasty as a treatment for coa is increasingly performed, with endovascular stents having been proposed as a means of improving the efficacy and safety of the procedure. the aim of this study was to evaluate the systolic blood pressure gradient at rest and during maximal e...

preaxial polydactyly is the most common duplication pattern in white and asian populations (1). it is a congenital anomaly with a wide range of manifestations .current classification do not have the capacity to classify all different types of radial polydactyly. we describe here a very rare and unusual case of bilateral preaxial polydactyly (triplication) in a woman and report the operations re...