نتایج جستجو برای: facial dysmorphism

تعداد نتایج: 60752  

2016
Qian Jiang Tao Zhang Shuo Wang Ping Xiao Zhen Zhang Yinan Ma Wei Cheng Lin Su Hong Pan Qi Li Long Li

Mowat-Wilson syndrome (MWS, MIM #235730) is a rare genetic disorder characterized by moderate-tosevere mental retardation, a recognizable facial gestalt and multiple congenital anomalies. The striking facial phenotype in addition to other features such as microcephaly, congenital heart defects, Hirschsprung disease (HSCR), severely delayed motor/speech development, seizures, short stature, corp...

2018
Aida M. Mossaad Moustapha A. Abdelrahman Mostafa A. Ibrahim Hatem H. Al Ahmady

BACKGROUND Robinow Syndrome is an extremely rare genetic disorder characterised by abnormalities in head, face and external genitalia. This disorder exists in dominant pattern with moderate symptoms and recessive pattern with more physical and skeletal abnormalities. It was first introduced by Menihard Robinow in 1969. It was related to chromosome 9q22 ROR2 gene related to bone and cartilage gr...

Journal: :Folia medica 2011
Tanya T Kitova Masmoudi Aida Zghall Dorra Chelli Dalenda Soumeya Siala Gaigi

UNLABELLED Holoprosencephaly (HPE) is a congenital central nervous system malformation estimated to occur in 1/250 conceptuses and 1/10,000 live births. While the severe forms, which are incompatible with life, are easier to detect in the prenatal period, the milder forms can remain unrecognised. As this can have serious consequences for the pregnancy and malformation carriers it is of crucial ...

2017
Eitaro Hiejima Takahiro Yasumi Hiroshi Nakase Minoru Matsuura Yusuke Honzawa Hirokazu Higuchi Ikuo Okafuji Tohru Yorifuji Takayuki Tanaka Kazushi Izawa Tomoki Kawai Ryuta Nishikomori Toshio Heike

RATIONALE Tricho-hepato-enteric syndrome (THES) is a rare disorder caused by mutations in the TTC37 or SKIV2L genes and characterized by chronic diarrhea, liver disease, hair abnormalities, and high mortality in early childhood due to severe infection or liver cirrhosis. PATIENT CONCERNS The patient is the second child of three siblings born to non-consanguineous healthy Japanese parents. She...

Journal: :Orphanet Journal of Rare Diseases 2008
Olivier Goulet Christine Vinson Bertrand Roquelaure Nicole Brousse Christine Bodemer Jean-Pierre Cézard

Syndromic diarrhea (SD), also known as phenotypic diarrhea (PD) or tricho-hepato-enteric syndrome (THE), is a congenital enteropathy presenting with early-onset of severe diarrhea requiring parenteral nutrition (PN). To date, no epidemiological data are available. The estimated prevalence is approximately 1/300,000-400,000 live births in Western Europe. Ethnic origin does not appear to be assoc...

2017
Edoardo Casiglia Panagiota Rempelou Valérie Tikhonoff Margherita Giacomello Francesco Finatti Federica Albertini Jacopo Favaro Antonio M. Lapenta Enrico Facco

Hypnotic focused analgesia, comparable to chemical local anesthesia, has been widely documented in our Laboratory after hypnotic suggestions. This study is aimed at producing hypnotic local anesthesia suggesting that a hand does not belong to the body (body dysmorphism) without any direct suggestions of analgesia. Eight healthy, highly hypnotizable volunteers underwent a cold pressor test keepi...

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