نتایج جستجو برای: germline mutation

تعداد نتایج: 300136  

Journal: :Genetics and molecular research : GMR 2014
Z L Li H H Guan X M Xiao Y Hui W X Jia R X Yu H Chen C R Li

Trichoepithelioma is a benign neoplasm that primarily shows follicular germinative differentiation. Classic trichoepithelioma typically presents as a skin-colored papule or nodule on the face or upper trunk; lesions have a predilection for the nose. Trichoepithelioma can be sporadic or familial and solitary or multiple. Most previously reported multiple trichoepithelioma cases are familial, and...

2016
Jon M. Steichen Daniel W. Kulp Talar Tokatlian Amelia Escolano Pia Dosenovic Robyn L. Stanfield Laura E. McCoy Gabriel Ozorowski Xiaozhen Hu Oleksandr Kalyuzhniy Bryan Briney Torben Schiffner Fernando Garces Natalia T. Freund Alexander D. Gitlin Sergey Menis Erik Georgeson Michael Kubitz Yumiko Adachi Meaghan Jones Andrew A. Mutafyan Dong Soo Yun Christian T. Mayer Andrew B. Ward Dennis R. Burton Ian A. Wilson Darrell J. Irvine Michel C. Nussenzweig William R. Schief

Broadly neutralizing antibodies (bnAbs) against the N332 supersite of the HIV envelope (Env) trimer are the most common bnAbs induced during infection, making them promising leads for vaccine design. Wild-type Env glycoproteins lack detectable affinity for supersite-bnAb germline precursors and are therefore unsuitable immunogens to prime supersite-bnAb responses. We employed mammalian cell sur...

2013
Young Sik Choi Hye Jung Kwon Bu Kyung Kim Su Kyoung Kwon Yo Han Park Jeong Hoon Kim Sang Bong Jung Chang Hoon Lee Seong Keun Lee Shinya Uchino

Many cases of RET proto-oncogene mutations of hereditary medullary thyroid carcinoma (MTC) have been reported in Korea. However, MTC with V804M RET proto-oncogene germline mutations have not been reported in Korea. A 33-yr-old man was diagnosed with a 0.7-cm sized thyroid nodule. Laboratory testing revealed serum calcitonin was elevated. The patient underwent total thyroidectomy with central co...

Journal: :Journal of medical genetics 1999
J T Celebi H C Tsou F F Chen H Zhang X L Ping M G Lebwohl J Kezis M Peacocke

Cowden syndrome (CS) and Bannayan-Zonana syndrome (BZS) are two hamartoma syndromes with distinct phenotypic features. Although partial clinical overlap exists between CS and BZS, they are considered to be separate entities. PTEN has been identified as the susceptibility gene for both disorders, suggesting allelism. We have identified a germline mutation, R335X, in PTEN in a family consisting o...

2013
Albino Bacolla Nuri A. Temiz Ming Yi Joseph Ivanic Regina Z. Cer Duncan E. Donohue Edward V. Ball Uma S. Mudunuri Guliang Wang Aklank Jain Natalia Volfovsky Brian T. Luke Robert M. Stephens David N. Cooper Jack R. Collins Karen M. Vasquez

Single base substitutions constitute the most frequent type of human gene mutation and are a leading cause of cancer and inherited disease. These alterations occur non-randomly in DNA, being strongly influenced by the local nucleotide sequence context. However, the molecular mechanisms underlying such sequence context-dependent mutagenesis are not fully understood. Using bioinformatics, computa...

2006
Ling Xia Wei Shen Frank Ritacca Angela Mitri Lisa Madlensky Terri Berk Zane Cohen Steven Gallinger Bharati Bapat

Germline mutations of the hit SI 12 gene are responsible for many cases of hereditary nonpolyposis colorectal cancer. While screening for HMSH2 gene mutations in hereditary nonpolyposis colorectal cancer kindreds, we observed that a previously reported germline mutation is in fact a com mon, alternatively spliced variant in the population. Using RT-PCR and the protein truncation test, the hMSH2...

Journal: :Blood 2000
D Dilworth L Liu A K Stewart J R Berenson N Lassam D Hogg

Germline mutations of the CDKN2A (p16(INK4A)) tumor suppressor gene predispose patients to melanoma and pancreatic carcinoma. In contrast, mutations of the murine CDKN2A gene predispose BALB/c mice to pristane-induced plasmacytoma. We describe here a family in which a germline mutation of CDKN2A is present in 4 individuals who developed melanoma as well as in a fifth family member who is suffer...

Journal: :Cancer research 1995
E A Strauss M R Hosler P Herzog K Salhany R Louie C A Felix

We demonstrated a germline p53 replication error in two generations of a Li-Fraumeni family affected with liposarcoma, adrenocortical carcinoma, and osteosarcoma. The trinucleotide repeat mutation changed 5'-AGT GTG GTG GTG-3' at codons 215-218 to 5'-AGT TGG TTG GTG GTG-3'. The predicted protein would be elongated by one amino acid (val216-->trp leu) without a change in charge. Detection of p53...

Journal: :The American Journal of Human Genetics 2007

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