نتایج جستجو برای: hypogonadotropic hypogonadism

تعداد نتایج: 3749  

Journal: :The Journal of clinical endocrinology and metabolism 2002
Roberto Salvi Fulgencio Gomez Muriel Fiaux Daniel Schorderet J Larry Jameson John C Achermann Rolf C Gaillard François P Pralong

DAX-1 [dosage-sensitive sex reversal, adrenal hypoplasia congenital (AHC) critical region on the X chromosome, gene 1] is a transcription factor expressed in the adrenal gland and at all levels of the gonadotrope axis. Inactivating mutations of DAX1 result in the X-linked form of AHC with associated hypogonadotropic hypogonadism. AHC usually reveals itself as adrenal failure in early infancy, a...

2016
Faycal El Guendouz Ahmed Gaouzi

Congenital hypogonadotropic hypogonadism (CHH) is an insufficient production of sex hormones due to loss of hypothalamic–pituitary–gonadal axis control. it is referred to as combined deficiency when it is associated with impairment of other endocrine axes. Signs of congenital hypogonadotropic hypogonadism are micro penis, delayed puberty in adolescence and infertility in adulthood. Abnormal sex...

Journal: :The Journal of clinical endocrinology and metabolism 2005
Nelly Pitteloud James S Acierno Astrid U Meysing Andrew A Dwyer Frances J Hayes William F Crowley

Kallmann syndrome (KS) is a clinically and genetically heterogeneous disorder. Recently, loss-of-function mutations in the fibroblast growth factor receptor 1 (FGFR1) gene have been shown to cause autosomal dominant KS. To date, the detailed reproductive phenotype of KS associated with mutations in the FGFR1 has yet to be described. We report a kindred comprising a male proband with KS and spon...

2015
Barbara Witek Abeer El Wakil Christoffer Nord Ulf Ahlgren Maria Eriksson Emma Vernersson-Lindahl Åslaug Helland Oleg A. Alexeyev Bengt Hallberg Ruth H. Palmer

Mice lacking ALK activity have previously been reported to exhibit subtle behavioral phenotypes. In this study of ALK of loss of function mice we present data supporting a role for ALK in hypogonadotropic hypogonadism in male mice. We observed lower level of serum testosterone at P40 in ALK knock-out males, accompanied by mild disorganization of seminiferous tubules exhibiting decreased numbers...

Journal: :The Journal of clinical investigation 2008
John Falardeau Wilson C J Chung Andrew Beenken Taneli Raivio Lacey Plummer Yisrael Sidis Elka E Jacobson-Dickman Anna V Eliseenkova Jinghong Ma Andrew Dwyer Richard Quinton Sandra Na Janet E Hall Celine Huot Natalie Alois Simon H S Pearce Lindsay W Cole Virginia Hughes Moosa Mohammadi Pei Tsai Nelly Pitteloud

Idiopathic hypogonadotropic hypogonadism (IHH) with anosmia (Kallmann syndrome; KS) or with a normal sense of smell (normosmic IHH; nIHH) are heterogeneous genetic disorders associated with deficiency of gonadotropin-releasing hormone (GnRH). While loss-of-function mutations in FGF receptor 1 (FGFR1) cause human GnRH deficiency, to date no specific ligand for FGFR1 has been identified in GnRH n...

Journal: :Endocrine journal 2010
Andrew Advani Sarah J Johnson Moira R Nicol Georgia Papacleovoulou Dean B Evans Suresh Vaikkakara J Ian Mason Richard Quinton

Estrogen-secreting adrenal cancers are extremely rare, with feminizing symptoms attributed to aromatase expression in the adrenal tumor. We describe a case of hypogonadotropic hypogonadism as a consequence of aberrant aromatase expression in a patient with adrenocortical adenocarcinoma. A 54 year-old man presented with a two month history of gynecomastia and reduced libido. Endocrine biochemist...

2016
Ana Rita Gomes Pedro Souteiro Carolina Germana Silva Bernardo Sousa-Pinto Francisco Almeida António Sarmento Davide Carvalho Paula Freitas

BACKGROUND The prevalence of hypogonadism in HIV-infected patients is still a matter of debate as there is no standardized consensual diagnostic method. In addition, the etiology and endocrine/metabolic implications of hypogonadism in this population remain controversial. This study aims to determine the prevalence of testosterone deficiency in a single-site hospital and to evaluate its associa...

Journal: :The Egyptian Journal of Hospital Medicine 2021

Background: Thalassemia is the most common cause of chronic hemolytic anemia and correlated with significant morbidity mortality. Osteoprotegerin (OPG) an ? tumor necrosis factor receptor superfamily glycoprotein that acts as a decoy for activator nuclear kappa B ligand (RANKL), exerting antiresorptive bone effect also play critical roles in hypogonadism associated osteoporosis. Objective: Toe...

Masoud Amini, Mehrdad Hosein Pour,

SUMMARY We studied the chronic effect of chemical gases on pituitary-gonad axis of victims of Iran and Irag war. The patients that their poisoning were higher than three years, selected. After clinical evaluation, and role out of systemic disease 168 victims were tested for testosterone, follicular stimulating hormone and leutinizing hormone. Comparison of results control group (n=200) and wi...

2017
Justin Chosich Andrew P. Bradford Amanda A Allshouse Jane E. B. Reusch Nanette Santoro Irene E Schauer

OBJECTIVE To determine the effect of lipid/heparin versus saline infusion, with or without concurrent euglycemic hyperinsulinemia, on serum follicle-stimulating hormone (FSH) and luteinizing hormone (LH). Obesity is associated with hyperlipidemia, insulin resistance, and relative hypogonadotropic hypogonadism. It was hypothesized that acutely elevated fatty acids and insulin would impair gonado...

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