نتایج جستجو برای: link recessive

تعداد نتایج: 212740  

Journal: :The Journal of clinical investigation 2015
William F Pendergraft Terry K Means

Systemic lupus erythematosus (SLE) is a severe autoimmune disease characterized by the presence of nucleic acid- and protein-targeting autoantibodies and an aberrant type I IFN expression signature. Aicardi-Goutières syndrome (AGS) is an autosomal-recessive encephalopathy in children that is characterized by mutations in numerous nucleic acid repair enzymes and elevated IFN levels. Phenotypical...

Journal: :The Journal of biological chemistry 2010
Rossana Foti Silvia Zucchelli Marta Biagioli Paola Roncaglia Sandra Vilotti Raffaella Calligaris Helena Krmac Javier Enrique Girardini Giannino Del Sal Stefano Gustincich

Mutations in PARK7/DJ-1 are associated with autosomal recessive, early onset Parkinson disease (PD). DJ-1 is an atypical peroxiredoxin-like peroxidase that may act as a redox-dependent chaperone and a regulator of transcription. Here we show that DJ-1 plays an essential role in the expression of rearranged during transfection (RET), a receptor for the glial cell line-derived neurotrophic factor...

2007
Moe Tategu Takako Arauchi Rena Tanaka Hiroki Nakagawa Kenichi Yoshida

Fanconi anemia (FA) is an autosomal recessive disorder characterized by congenital abnormalities, bone marrow failure, chromosome fragility, and cancer susceptibility. At least eleven members of the FA gene family have been identified using complementation experiments. Ubiquitin-proteasome has been shown to be a key regulator of FA proteins and their involvement in the repair of DNA damage. Her...

Journal: :Cell 2007
Sandra M. Siepka Seung-Hee Yoo Junghea Park Weimin Song Vivek Kumar Yinin Hu Choogon Lee Joseph S. Takahashi

Using a forward genetics ENU mutagenesis screen for recessive mutations that affect circadian rhythmicity in the mouse, we isolated a long period (approximately 26 hr) circadian mutant named Overtime (Ovtm). Positional cloning and genetic complementation reveal that Ovtm is encoded by the F-box protein FBXL3, a component of the SKP1-CUL1-F-box-protein (SCF) E3 ubiquitin ligase complex. The Ovtm...

Journal: :Journal of Neuropathology & Experimental Neurology 2005

Journal: :Journal of Applied Biomedicine 2004

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