THE association of buphthalmos with facial naevus has received attention in ophthalmological literature from time to time over a period of many years, and a recent revival of interest in the subject has been stimulated by the appearance of articles by Cushing, Parkes WVeber, Aynsley and others. About the time of the appearance of Aynsley's paper the following very early case came under my notic...

A 71-year-old woman with the blue rubber bleb naevus syndrome experienced 4 episodes of self-limiting unilateral exophthalmos. Is is suggested that a vascular malformation in the orbit is responsible for this phenomenon. A biopsy sample was taken of one of the cutaneous lesions and studied by light and transmission electron microscopy. The histological appearances are discussed in relation to p...

A case of basal cell naevus syndrome is presented. The jaw cysts were proved histopathologically to be odontogenic keratocysts. The multiple naevoid lesions on the skin were identified as basal cell carcinoma. Intracranial calcification is illustrated to a degree not previously reported in a case with this syndrome. The importance of identifying this syndrome is discussed and its presentation i...