نتایج جستجو برای: adrenoleukodystrophy

تعداد نتایج: 2020  

2013
Chul-Yong Park Han-Soo Kim Jiho Jang Hyunji Lee Jae Souk Lee Jeong-Eun Yoo Dongjin R. Lee Dong-Wook Kim

X-linked adrenoleukodystrophy (X-ALD) is a peroxisomal disorder caused by mutations in the ABCD1 gene that encodes the peroxisomal ATP-binding cassette (ABC) transporter subfamily D member 1 protein (ABCD1), which is referred to as the adrenoleukodystrophy protein (ALDP). Induction of the ABCD2 gene, the closest homolog of ABCD1, has been mentioned as a possible therapeutic option for the defec...

2011
Neeraj Kumar Krishna Kant Taneja Veena Kalra Madhuri Behari Satinder Aneja Surendra Kumar Bansal

X-linked adrenoleukodystrophy (X-ALD) affects the nervous system white matter and adrenal cortex secondary to mutations in the ABCD1 gene that encode the peroxisomal membrane protein. We conducted a genomic and protein expression study of susceptibility gene with its clinical and biochemical analysis. To the best of our knowledge this is the first preliminary comprehensive study in Indian popul...

Journal: :Clinical & Biomedical Research 2021

Introduction: Several studies in the literature have evaluated role of oxidative stress and adjuvant therapies for X-linked adrenoleukodystrophy (X-ALD). Here, we investigated whether n-acetyl-L-cysteine (NAC) rosuvastatin (RSV) could influence generation reactive species, redox status nitrative fibroblasts from asymptomatic patients with X-ALD. Methods: Skin biopsy samples were cultured treate...

نمودار تعداد نتایج جستجو در هر سال

با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید