نتایج جستجو برای: chiari syndrome
تعداد نتایج: 623818 فیلتر نتایج به سال:
The association of Budd-Chiari Syndrome (BCS) with coeliac disease has been understudied and underreported. Majority the cases this have reported from North Africa Southern Europe, due to a higher prevalence disease. BCS can present as acute, subacute, or chronic form is characterised by hepatic venous obstruction, either thrombotic non-thrombotic without any evidence sinusoidal obstruction syn...
This study investigates whether the degree of brainstem herniation and the nature of the cervicomedullary deformity seen on sagittal plane MR images correlates with the clinical syndrome in patients with the Chiari II malformation. The amount of brainstem herniation was assessed by relating the position of the midbrain and pons to the sella turcica and the anterior lip of the foramen magnum, re...
We report on the case of two young patients with type I Arnold-Chiari malformation (ACM), as revealed by a central sleep apnoea (CSA) syndrome without any other neurological defect. Case 1 was a 14-yr-old male patient, who developed severe alveolar hypoventilation and needed long-term mechanical ventilation via a tracheostomy. Case 2 was a 39-yr-old male patient, who developed features suggesti...
This article reports the largest familial aggregation of Chiari malformation in a single family to date as reported in the literature. This study is a retrospective case series of a family of whom five individuals have a confirmed case of Chiari malformation and three additional individuals have Chiari signs and symptoms. This contribution further supports the implication of genetics in the tra...
BACKGROUND Behcet's disease (BD) is a well-known cause of Budd-Chiari syndrome (BCS). Data are lacking on the presentation and outcome of BCS related to BD. METHODS We investigated the relationship between BD and BCS in 14 patients with both diseases and compared the results to 92 BCS patients without BD. RESULTS Male gender (p = 0.003), North African origin (P = 0.007) and inferior vena ca...
Sir, Mahmoud ef a/. have recently reported underlying myeloproliferative disorders (MPD) as the commonest aetiology in Budd-Chiari syndrome (BCS) in their series. There appears to be continuing controversy over the aetiological factors and their geographical variation observed in this disorder. Earlier studies from Western countries have documented polycythemia vera as the commonest aetiology, ...
1. Méndez T, Otero I, García R, Pérez B. Síndrome de Klippel-Trenaunay-Weber: presentación de un caso. Rev Cubana Oftalmol. 2001;14:47-9. 2. Bordel MT, Miranda A. Un caso atípico de síndrome de Klippel-Trenaunay. Piel. 2005;20:306-8. 3. Gimeno P, Pérez P, López-Pisón J, Romeo M, Galeano N, Marco M, et al. Síndrome de Klippel-Trenaunay: a propósito de tres nuevas observaciones. An Esp Pediatr. 2...
نمودار تعداد نتایج جستجو در هر سال
با کلیک روی نمودار نتایج را به سال انتشار فیلتر کنید