نتایج جستجو برای: clinical exome sequencing

تعداد نتایج: 1271061  

Journal: :Deutsches Aerzteblatt Online 2019

   Background & Objective:  Peroxisome biogenesis disorders (PBDs) are a group of diseases with peroxisomal dysfunction. Wide range of symptoms are associated with the disease which are due to mutations in the PEX genes. The PEX1 mutation occurs in Zellweger syndrome (ZS), a severe autosomal recessive condition with hypotonia, intellectual disability, and hepatic enlargement. The present study ...

Journal: :Egyptian Journal of Medical Human Genetics 2022

Abstract Background Leydig cell hypoplasia (LCH) is a rare autosomal recessive endocrine syndrome that affects the normal development of male external genitalia in 46, XY individuals and one causes disorder sexual differentiation (DSD) males. The responsible gene LCH LHCGR which located on chromosome 2 its various mutations lead to different degrees disease ranging from micropenis complete DSD....

Journal: :Muscle & nerve 2013
Rabia Chaudhry Aditi Kidambi Megan Hwa Brewer Anthony Antonellis Katherine Mathews Garth Nicholson Marina Kennerson

INTRODUCTION Charcot-Marie-Tooth (CMT) disease is a group of peripheral neuropathies affecting both motor and sensory nerves. CMTX3 is an X-linked CMT locus, which maps to chromosome Xq26.3-q27.3. Initially, CMTX3 was mapped to a 31.2-Mb region in 2 American families. We have reexamined 1 of the original families (US-PED2) by next generation sequencing. METHODS Three members of the family und...

2016
Anne Bruun Krøigård Mads Thomassen Anne-Vibeke Lænkholm Torben A. Kruse Martin Jakob Larsen

Next generation sequencing is extensively applied to catalogue somatic mutations in cancer, in research settings and increasingly in clinical settings for molecular diagnostics, guiding therapy decisions. Somatic variant callers perform paired comparisons of sequencing data from cancer tissue and matched normal tissue in order to detect somatic mutations. The advent of many new somatic variant ...

2012
Alberto Gonzalez-Aguilar Ahmed Idbaih Blandine Boisselier Naïma Habbita Marta Rossetto elie Bruno Anne Jouvet Marc Polivka Clovis Adam Dominique Figarella-Branger Catherine Miquel Anne Vital Vincent Delwail Luc Taillandier Olivier Chinot Pierre Soubeyran Emmanuel Gyan Sylvain Choquet Caroline Houillier Carole Soussain Marie-Laure Tanguy Yannick Marie Karima Mokhtari Khê Hoang-Xuan

Purpose: Our objective was to identify the genetic changes involved in primary central nervous system lymphoma (PCNSL) oncogenesis and evaluate their clinical relevance. Experimental Design: We investigated a series of 29 newly diagnosed, HIV-negative, PCNSL patients usinghigh-resolution single-nucleotide polymorphism (SNP) arrays (n1⁄429) andwhole-exome sequencing (n1⁄4 4) approaches. Recurren...

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