supravalvar mitral ring is a rare congenital heart defect of surgical importance. the condition is characterized by an abnormal ridge of the connective tissue on the atrial side of the mitral valve. it often substantially obstructs the mitral valve inflow. we herein introduce a case of a supravalvar mitral ring in a 17-year-old male, who was admitted to our hospital with cardiac syncope. he had...

background: hypoalbuminemia may be caused by liver disease, nephrotic syndrome, burns, protein-losing entropathy, malnutrition, and metabolic stress. alterations in albumin in metabolic stress such as cardiac surgery have been previously investigated. we studied serum albumin concentration in children with congenital heart disease and also the association of hypoalbuminemia with mortality and m...

background: coarctation of the aorta (coa) is a defect that accounts for 5-8% of all congenital heart diseases. balloon angioplasty as a treatment for coa is increasingly performed, with endovascular stents having been proposed as a means of improving the efficacy and safety of the procedure. the aim of this study was to evaluate the systolic blood pressure gradient at rest and during maximal e...

conclusions children with chd are at risk of severe complications with the involvement of other organs. long-term febrile illness should be taken seriously in these children. they need hospitalization and careful evaluation. case presentation a 6-year-old girl with a ventricular septal defect (vsd) was presented. echocardiography revealed large vegetation in the right ventricular outflow tract ...

DURING the repair of congenital defects of the venitricular septum, various disturbances of cardiac function may occur.1'Permanent complete heart block has been the most serious of these disturbances. Right bundle-branch block seems benign. Inereased knowledge of the anatomic features of the atrioventricular (AV) conduction system has resulted in surgical technics that have nearly eliminated co...

The incidence of congenital atrioventricular (AV) block is estimated to be about 1 in 15,000-20,000 births. Although it is a rare disease, it increases fetal, neonatal, and childhood morbidity and mortality, and 60%-65% of all cases are reported to require pacemaker implantation before reaching adulthood (1). This disease can be idiopathic, but it is mostly caused by transmission of auto-antibo...

DURING the repair of congenital defects of the venitricular septum, various disturbances of cardiac function may occur.1'Permanent complete heart block has been the most serious of these disturbances. Right bundle-branch block seems benign. Inereased knowledge of the anatomic features of the atrioventricular (AV) conduction system has resulted in surgical technics that have nearly eliminated co...

Neonatal lupus erythematosus is an autoimmune disease produced by the passage of maternal antinuclear antibodies and extractable nuclear antigen antibodies through the placenta. At the moment of the diagnosis, the mothers are asymptomatic in 40 to 60% of cases. The most common manifestations are cutaneous lesions and congenital heart block. The cutaneous findings are variable and usually begin ...

BACKGROUND Autoimmune fetal congenital heart block (CHB) is the most severe manifestation of neonatal lupus, and it is seen when maternal autoimmune antibodies cross the placenta and damage the AV node of the fetus. CHB is mainly associated with maternal SLE with anti-Ro/SSA- and anti-La/SSB-positive status, and incidence of CHB increases when both the antibodies are present. This study was con...