Anderson-Kestenbaum operations for congenital nystagmus with severe head turn have been employed for the past 25 years. They have been documented as being effective in correcting head turns associated with congenital nystagmus. We have studied a group of patients with congenital nystagmus and head turn, both preoperatively and postoperatively, by means of recordings of eye movements. We have do...

We report a patient with acute cerebral infarction of the left paramedian thalamus, upper mesencephalon and cerebellum who exhibited ipsilateral oculomotor nerve palsy and contralateral downbeat nystagmus. The site of the infarction was considered to be the paramedian thalamopeduncular and cerebellar regions, which are supplied by the superior cerebellar artery containing direct perforating bra...

Some pharmacological effects of a potent tremorgenic mycotoxin, fumitremorgin A (FTA), on the rabbit were studied. FTA (10-200 micrograms/kg, i.v.) caused clonic and tonic convulsion accompanied by nystagmus and miosis in conscious rabbits, after a latent period. Even in decorticated or decerebrated rabbits, FTA (100-200 micrograms/kg, i.v.) could induce violent motor effects similar to those o...

SUM MARY Direct current electronystagmographic recordings of spontaneous nystagmus in light, in darkness, and with eye closure have been carried out on (a) 33 patients with acoustic neurinomata pressing on the brain stem, and (b) 10 patients with lesions involving the brain stem at a high level. Patterns of response characteristics of each group have been identified in 21 out of 28 cases of gro...

Superior canal dehiscence syndrome is a newly recognized syndrome characterized by vertigo and nystagmus induced by sound (Tullio phenomenon) or changes of middle ear (Hennebert sign) or intracranial pressure. We report on a patient with bilateral superior canal dehiscence syndrome who presented with unusual manifestations including pulse-synchronous vertical pendular nystagmus and Valsalva-ind...

The electronystagmographic auditory brainstem response and magnetic resonance imaging findings for a 33-year-old male with a 3.5 cm left vestibular schwannoma are presented. Of particular interest was the presence of an unusual positioning nystagmus following the Dix-Hallpike maneuver in the right head-hanging position. The patient demonstrated a nystagmus that was immediate in onset and not fa...

OBJECTIVE To test the hypothesis that the extraocular muscles (EOMs) of patients with infantile nystagmus have muscular and innervational adaptations that may have a role in the involuntary oscillations of the eyes. METHODS Specimens of EOMs from 10 patients with infantile nystagmus and postmortem specimens from 10 control subjects were prepared for histologic examination. The following varia...

THERE ARE TWO FORMS OF LATERAL SEMICIRCULAR CANAL BENIGN PAROXYSMAL POSITIONAL VERTIGO: geotropic and apogeotropic. When the pathophysiological mechanism of the apogeotropic form is that of canalolithiasis, we can observe a transformation from an apogeotropic nystagmus into a geotropic one. Usually, this phenomenon happens simultaneously on both sides, thus enabling us to observe a right-beatin...

Introduction. Laurence-Moon-Biedl (LMB) syndrome is a rare autosomal-recessive ciliopathy with manifold symptomatology. The cardinal clinical features include retinitis pigmentosa, obesity, intellectual delay, polydactyly/syndactyly, and hypogenitalism. In this paper, the authors report on three siblings with Laurence-Moon-Biedl syndrome associated with a probable pseudocycloid form of congenit...

The Southern California Sensory Integration Test results of 109 learning-disabled children were reviewed and analyzed to investigate the hypothesis that learning-disabled children with excessive postrotary nystagmus durations display greater neuropsychological impairment than learning-disabled children with normal or depressed postrotary nystagmus. The findings supported the hypothesis that lea...