congenital defects of the pericardium are considered rare. until 1979 , the reported cases were only about 200.1 total absence of the left pericardium is the most common defect2 and less common is a partial defect of the left pericardium. other types, i.e. isolated right-sided defects, total pericardial absence and diaphragmatic pericardial defects are very rare.3 before the last decade, the di...