نتایج جستجو برای: premature craniosynostosis

تعداد نتایج: 62797  

Journal: :The Cleft palate-craniofacial journal : official publication of the American Cleft Palate-Craniofacial Association 2014
Sun-Don Kim Garima Yagnik Michael L Cunningham Jinoh Kim Simeon A Boyadjiev

OBJECTIVE The MAPK/ERK signaling pathway has been implicated in several craniosynostosis syndromes and represents a plausible target for therapeutic management of craniosynostosis. The causes of sagittal nonsyndromic craniosynostosis (sNSC) have not been well understood and the role that MAPK/ERK signaling cascade plays in this condition warrants an investigation. We hypothesized that MAPK-sign...

Journal: :Pediatrics 2014
Marianne Maliepaard Irene M J Mathijssen Jaap Oosterlaan Jolanda M E Okkerse

OBJECTIVES To examine intellectual, behavioral, and emotional functioning of children who have syndromic craniosynostosis and to explore differences between diagnostic subgroups. METHODS A national sample of children who have syndromic craniosynostosis participated in this study. Intellectual, behavioral, and emotional outcomes were assessed by using standardized measures: Wechsler Intelligen...

2014
Hyun Gee Ryoo Seung-Ki Kim Jung-Eun Cheon Ji Yeoun Lee Kyu-Chang Wang Ji Hoon Phi

PATIENT Female, 14 months FINAL DIAGNOSIS Slit ventricle syndrome Symptoms: Hydrocephalus • lethargy and seizure • vomiting MEDICATION - Clinical Procedure: - Specialty: Pediatrics and Neonatology. OBJECTIVE Challenging differential diagnosis. BACKGROUND Shunt surgery is a common solution for hydrocephalus in infancy. Slit ventricle syndrome and secondary craniosynostosis are late-onset...

Journal: :Plastic and Reconstructive Surgery - Global Open 2019

Journal: :Journal of Neurosciences in Rural Practice 2016

Journal: :Neurosurgical Focus 1997

Journal: :Journal of medical genetics 2006
L Van Maldergem H A Siitonen N Jalkh E Chouery M De Roy V Delague M Muenke E W Jabs J Cai L L Wang S E Plon C Fourneau M Kestilä Y Gillerot A Mégarbané A Verloes

Baller-Gerold syndrome (BGS) is a rare autosomal recessive condition with radial aplasia/hypoplasia and craniosynostosis (OMIM 218600). Of >20 cases reported so far, a few appear atypical and have been reassigned to other nosologic entities, including Fanconi anaemia, Roberts SC phocomelia, and Pfeiffer syndromes after demonstration of corresponding cytogenetic or molecular abnormalities. Clini...

2017
Ying Lin Hongbin Gao Siming Ai Jacob V.P. Eswarakumar Chuan Chen Yi Zhu Tao Li Bingqian Liu Xialin Liu Lixia Luo Hongye Jiang Yonghao Li Xiaoling Liang Chenjin Jin Xinhua Huang Lin Lu

The current study was performed with aim to investigate the fibroblast growth factor receptor 2 (FGFR2) gene in two Chinese families with two different forms of syndromic craniosynostosis, and to characterize their associated clinical features. Two families underwent complete ophthalmic examinations, and two patients from each family were diagnosed with craniosynostosis. Genomic DNA was extract...

2017
YING LIN HONGBIN GAO CHUAN CHEN YI ZHU TAO LI BINGQIAN LIU XIALIN LIU LIXIA LUO HONGYE JIANG YONGHAO LI XIAOLING LIANG CHENJIN JIN XINHUA HUANG

The current study was performed with aim to investigate the fibroblast growth factor receptor 2 (FGFR2) gene in two Chinese families with two different forms of syndromic craniosynostosis, and to characterize their asso‐ ciated clinical features. Two families underwent complete ophthalmic examinations, and two patients from each family were diagnosed with craniosynostosis. Genomic DNA was extra...

Journal: :Neurosurgical Focus 2021

OBJECTIVE The advent of endoscopic synostectomy has enabled early surgery for infants with craniosynostosis. Even though diagnosis is often made at birth, traditionally been delayed until the infant 3 months age. There have very few published reports this procedure being performed in neonatal period. authors discuss their experience ultra-early synostectomy, defined as an operation aged 8 weeks...

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