Hydroxychloroquine-induced cardiomyopathy is a rare adverse reaction with serious and potentially fatal outcomes. We report 56-year-old female who presented in acute right heart failure NYHA class III symptoms, ascites, raised JVP pressure, peripheral oedema. Significant medical history included SLE (diagnosed her late 20s, well controlled on hydroxychloroquine), CKD, poorly hypertension. Exten...

A patient with pseudoxanthoma elasticum presented in pulmonary oedema with restrictive left ventricular cardiomyopathy caused by calcified endocardial bands that were confirmed on echocardiography and at catheterisation. The bands were resected as far as possible and the involved mitral valve was replaced by a heterograft. A year later calcification of the heterograft forced its replacement by ...

1. Lang R, David D, Klein HO, et al. The use of the balloon-tipped floating catheter in temporary transvenous cardiac pacing. Pacing Clin Electrophysiol 1981;4:491–6. 2. Trigano JA, Birkui PJ, Mugica J. Noninvasive transcutaneous cardiac pacing: modern instrumentation and new perspectives. Pacing Clin Electrophysiol 1992;15:1937–43. 3. Asano M, Mishima A, Ishii T, Takeuchi Y, Suzuki Y, Manabe T...

A57-year-old woman had a history of idiopathic hypereosinophilic syndrome (previously treated with hydroxyurea) and recent progression to myelodysplastic syndrome. She presented with 6 months of fatigue, 2 months of progressive dyspnea on exertion and orthopnea, a 10-pound weight gain, and increased abdominal girth. On admission, she appeared chronically ill and had tachycardia, jugular venous ...

Endomyocardial fibrosis (EMF) is a distinct obliterative cardiomyopathy characterized anatomically by right/left/bi ventricular endocardial fibrotic thickening and varying degrees of obliteration of the ventricular cavity. Chamber obliteration leads to diastolic restriction to ventricular filling and thus diastolic ventricular dysfunction. Involvement of the chordae tendinae and papillary muscl...

Familial cardiac conduction disorder of a progressive nature has been reported in adult and paediatric patients. An underlying cardiomyopathy was found in most of these patients, either of hypertrophic, restrictive or dilated variety. Systemic diseases like juvenile rheumatoid arthritis and other collagen disorders and familial dysautonomia infrequently have associated conduction abnormalities....

Embolic cerebral infarction due to cardiac amyloidosis is rare. We report two patients with amyloidosis who developed cerebral infarcts. These embolic infarcts were probably related to cardiac involvement of amyloidosis, which was based on results of myocardial biopsy (Patient 1), and kidney biopsy and characteristic echocardiographic features including granular sparkling, restrictive cardiomyo...