Hypoplasia of the right ventricle, unassociated with severe pulmonary or tricuspid valvar malformations, is a primary congenital abnormality in which the trabeculated sinus portion of the ventricle fails to develop. An atrial septal defect or a stretched foramen ovale serves as an escape valve. The clinical, hemodynamic, and angiocardiographic features of this rare type of cyanotic heart diseas...

rom the University School f Medicine, Clinical Center f Serbia, Cardiology Clinic nd Emergency Hospital, oronary Care Unit, elgrade, Serbia. anuscript received ebruary 10, 2010; ccepted February 18, 2010. A49-year-old woman presented to the emergency department with dyspnea 3 days after her mother’s death. The electrocardiogram at admission showed sinus tachycardia, T-wave inversion in leads V1...

Right ventricular growth was assessed angiocardiographically in 18 patients with pulmonary atresia, intact ventricular septum, and hypoplastic and hypertensive right ventricle. A variety of surgical procedures were performed. In only 12 patients (66.7%) was right ventricular-pulmonary artery continuity achieved (group 1). Nine of these 12 patients persisted with systemic or suprasystemic right ...

THE GENESIS OF COMMUNICATIONS between the right ventricle and coronary arteries commonly associated with pulmonary atresia remains uncertain. Edwards' attributed the persistence of these communicating sinusoids to increased right ventricular pressure and emphasized the importance of right ventricular outflow obstruction, intact ventricular septum, and competence of the tricuspid valve. Other au...

Arrythmogenic right ventricular (RV) cardiomyopathy (ARVC) is a cardiomyopathy characterized pathologically by fibrofatty replacement primarily of the RV and clinically by life-threatening ventricular arrhythmias in apparently healthy young people. The prevalence of the disease has been estimated at 1 in 5,000 individuals, although this estimate will likely increase as awareness of the conditio...

Whilst failure of the left ventricle (LV) has been the subject of intense interest for decades, failure of the right ventricle (RV) has tended to receive scant attention. Indeed, the RV was long considered a relatively passive conduit for blood flow between the systemic and pulmonary circulations. More recently, the importance of the RV in maintaining haemodynamic stability and organ function h...

Fourteen patients with predominantly right sided dilated cardiomyopathy were studied, of whom five died suddenly. The condition is characterised by male preponderance, syncope, ventricular tachycardia, which typically has a left bundle branch block pattern on the surface electrocardiogram, and right heart failure. The diagnosis should be considered in patients presenting with otherwise unexplai...

Arritmogenic right ventricular dysplasia (ARVD) is characterized by the gradual replacement of myocytes by adipose and fibrous tissue. Described in 1977, is considered a potentially lethal cause of cardiac disease poorly understood. This disorder usually involves the right ventricle and has been associated with arrthymia, heart failure, and sudden death. In this paper, we report a case of a 25-...

Figure 1 (A and B) Right ventricular mass (arrowed) attached to the tricuspid valve chordae apparatus on echocardiography, in apical four-chamber view, and modified parasternal right ventricular inflow view respectively; (C and D) repeat echocardiogram demonstrating enlargement of the original mass and an additional mass (longer arrow), modified parasternal right ventricular i mass on computeri...