primary immunodeficiencies (pid) are a group of disorders, characterized by an unusual susceptibility to infections. delay in diagnosis results in increased morbidity and mortality in affected patients. the purpose of this study was to determine the mortality rate of iranian immunodeficient patients referred to children medical center hospital affiliated to tehran university of medical sciences...

V.P. Kubarovsky, N. Akchurin, V. A. Andreev, A.G. Atamantchouk, M. Aykac, M.Y. Balatz, N.F. Bondar, A. Bravar, M. Chensheng, P.S. Cooper, L.J. Dauwe, G.V. Davidenko, U. Dersch, A.G. Dolgolenko, D. Dreossi , G.B. Dzyubenko, R. Edelstein, A.M.F. Endler, J. Engelfried , C. Escobar, I. Eschrich, A.V. Evdokimov, T. Ferbel, I.S. Filimonov, F. Garcia , M. Gaspero , S. Gerzon, I. Giller , G. Ginther, V...

Late Miocene great ape crania are rare, mostly fragmentary, and the focus of much debate on great ape and human origins (Brown & Ward, 1988; Bonis et al., 1990; Moyà-Solà & Köhler, 1993, 1995; Begun, 1994; Kordos & Begun, 1997; Schwartz, 1997). Due to poor preservation, information on important features of cranial anatomy (facial angulation, prognathism, relative and absolute brain size) must b...

This paper considers the impact of ambiguity in strategic situations. It extends the existing literature on games with ambiguity-averse players by allowing for optimistic responses to ambiguity. We use the CEU model of ambiguity with a class of capacities introduced by Jaffray and Philippe (1997), which allows us to distinguish ambiguity from ambiguity-attitude, and propose a new solution conce...

Costs with dementia have been the focus of research around the world and indirect costs to the caregiver appear in the literature as responsible for the greatest impact. In Latin American (LA) studies, indirect costs with dementia range from 60% to 75% of family income. Objective To present preliminary results of the study "Description of the methods and cost analysis with dementia" currently...

superior vena cava (svc) syndrome is not an uncommon occurrence in patients with malignancy and it is often described as a medical emergency. in majority of the cases, svc syndrome occurs due to mechanical obstruction of the svc by extraluminal compression with primary intrathoracic malignancies. however, intraluminal obstruction due to thrombosis can also produce symptoms and signs of svc synd...

in this case report, we present the first diagnosed case of galloway- mowat syndrome in iran. a 7 month old infant boy with microcephaly that had prominently stunted head growth after birth, gastroesophageal reflux, multiple craniofascial characters, hypothyroidism and nephrotic syndrome diagnosed at 5 months of age associated with rapid decline in renal function and heavy proteinuria in 2 mont...